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List of works by David Palmer

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Mitochondrial ATP synthase subunit c storage in the ceroid-lipofuscinoses (Batten disease)

scientific article published on 01 February 1992
NCL disease mechanisms

scientific article published on 23 May 2013
Glial activation spreads from specific cerebral foci and precedes neurodegeneration in presymptomatic ovine neuronal ceroid lipofuscinosis (CLN6).

scientific article
Defective endoplasmic reticulum-resident membrane protein CLN6 affects lysosomal degradation of endocytosed arylsulfatase A

scientific article published on 21 May 2004
Ovine ceroid lipofuscinosis. The major lipopigment protein and the lipid-binding subunit of mitochondrial ATP synthase have the same NH2-terminal sequence

scientific article published on 01 April 1989
Lysine 43 is trimethylated in subunit C from bovine mitochondrial ATP synthase and in storage bodies associated with batten disease

scientific article published on 9 March 2004
Sheep and other animals with ceroid-lipofuscinoses: their relevance to Batten disease.

scientific article published in February 1992
A missense mutation (c.184C>T) in ovine CLN6 causes neuronal ceroid lipofuscinosis in Merino sheep whereas affected South Hampshire sheep have reduced levels of CLN6 mRNA.

scientific article published on 12 September 2006
Ceroid-lipofuscinosis (Batten's disease): pathogenesis and sequential neuropathological changes in the ovine model

scientific article published on 01 July 1989
A new large animal model of CLN5 neuronal ceroid lipofuscinosis in Borderdale sheep is caused by a nucleotide substitution at a consensus splice site (c.571+1G>A) leading to excision of exon 3.

scientific article
Batten disease and the ATP synthase subunit c turnover pathway: raising antibodies to subunit c.

scientific article published on 01 June 1995
Activation of non-neuronal cells within the prenatal developing brain of sheep with neuronal ceroid lipofuscinosis

scientific article published in April 2006
The neuronal ceroid-lipofuscinoses (Batten disease): comparative aspects

scientific article published on February 1995
Ceroid lipofuscinosis in sheep. II. The major component of the lipopigment in liver, kidney, pancreas, and brain is low molecular weight protein.

scientific article published in February 1986
Mapping quantitative trait loci (QTL) in sheep. I. A new male framework linkage map and QTL for growth rate and body weight

scientific article published on 24 April 2009
Location and connectivity determine GABAergic interneuron survival in the brains of South Hampshire sheep with CLN6 neuronal ceroid lipofuscinosis

scientific article published on 25 June 2008
Neuronal ceroid lipofuscinosis in Devon cattle is caused by a single base duplication (c.662dupG) in the bovine CLN5 gene

scientific article published on 25 July 2006
Different patterns of hydrophobic protein storage in different forms of neuronal ceroid lipofuscinosis (NCL, Batten disease)

scientific article published on 01 February 1997
Neuronal ceroid lipofuscinosis in Merino sheep

scientific article
Molecular neuropathology of the synapse in sheep with CLN5 Batten disease

scientific article
Lentiviral-mediated gene transfer to the sheep brain: implications for gene therapy in Batten disease.

scientific article
Enhanced expression of manganese-dependent superoxide dismutase in human and sheep CLN6 tissues

scientific article published on December 2003
Ceroid lipofuscinosis in sheep. I. Bis(monoacylglycero)phosphate, dolichol, ubiquinone, phospholipids, fatty acids, and fluorescence in liver lipopigment lipids

scientific article published on 01 February 1986
The origin of fluorescence in the neuronal ceroid lipofuscinoses (Batten disease) and neuron cultures from affected sheep for studies of neurodegeneration

scientific article published in May 2002
Neuronal ceroid-lipofuscinosis in Borderdale sheep

scientific article published in October 2002
Accumulation of sphingolipid activator proteins (SAPs) A and D in granular osmiophilic deposits in miniature Schnauzer dogs with ceroid-lipofuscinosis

scientific article
Ovine ceroid-lipofuscinosis. I: Lipopigment composition is indicative of a lysosomal proteinosis.

scientific article published on January 1988
Translational neurophysiology in sheep: measuring sleep and neurological dysfunction in CLN5 Batten disease affected sheep.

scientific article
Ion pores made of mitochondrial ATP synthase subunit c in the neuronal plasma membrane and Batten disease

scientific article published in April 1999
Metabolomic investigation of CLN6 neuronal ceroid lipofuscinosis in affected South Hampshire sheep

scientific article
Immunocytochemical studies in the ceroid-lipofuscinoses (Batten disease) using antibodies to subunit c of mitochondrial ATP synthase

scientific article published on 01 June 1995
Recent studies of ovine neuronal ceroid lipofuscinoses from BARN, the Batten Animal Research Network

scientific article
Longitudinal In Vivo Monitoring of the CNS Demonstrates the Efficacy of Gene Therapy in a Sheep Model of CLN5 Batten Disease

article
Ovine ceroid-lipofuscinosis II: Pathologic changes interpreted in light of biochemical observations

scientific article published on 01 January 1988
Changes in GABAergic neuron distribution in situ and in neuron cultures in ovine (OCL6) Batten disease

scientific article
Chronic oral administration of minocycline to sheep with ovine CLN6 neuronal ceroid lipofuscinosis maintains pharmacological concentrations in the brain but does not suppress neuroinflammation or disease progression

scientific article published on July 30, 2013
Disease-specific pathology in neurons cultured from sheep affected with ceroid lipofuscinosis

scientific article
In vitro culture of neurons from sheep with Batten disease

scientific article
Rapid and Progressive Regional Brain Atrophy in CLN6 Batten Disease Affected Sheep Measured with Longitudinal Magnetic Resonance Imaging

scientific article published on 10 July 2015
The development and characterisation of complex ovine neuron cultures from fresh and frozen foetal neurons

scientific article
The specific loss of GnRH-positive neurons from the hypothalamus of sheep with CLN6 neuronal ceroid lipofuscinosis occurs without glial activation and has only minor effects on reproduction

scientific article published on November 24, 2010
Inhibition of storage pathology in prenatal CLN5-deficient sheep neural cultures by lentiviral gene therapy.

scientific article published on 19 November 2013
Rapid, quantitative analysis of 3'- and 6'-sialyllactose in milk by flow-injection analysis-mass spectrometry: screening of milks for naturally elevated sialyllactose concentration

scientific article published on 17 October 2013
A triad of highly divergent polymeric immunoglobulin receptor (PIGR) haplotypes with major effect on IgA concentration in bovine milk

scientific article (publication date: 2013)
Splicing variants in sheep CLN3, the gene underlying juvenile neuronal ceroid lipofuscinosis

scientific article published in June 1999
Ceroid-lipofuscinosis in miniature Schnauzer dogs

scientific article published in January 1997
Computed tomography provides enhanced techniques for longitudinal monitoring of progressive intracranial volume loss associated with regional neurodegeneration in ovine neuronal ceroid lipofuscinoses

scientific article published on 23 August 2018
Neuropeptide changes and neuroactive amino acids in CSF from humans and sheep with neuronal ceroid lipofuscinoses (NCLs, Batten disease).

scientific article published on 05 August 2009
Variant proteins in ovine ceroid-lipofuscinosis

scientific article published on 01 June 1995
An EEG Investigation of Sleep Homeostasis in Healthy and CLN5 Batten Disease Affected Sheep.

scientific article published in August 2016

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