List of works - Brian S Appleby

A Practical Primer on Prion Pathology

scientific article published on 01 May 2018

A Review: Treatment of Alzheimer’s Disease Discovered in Repurposed Agents ⬇️

scientific article published on 09 January 2013

A case report of genetic prion disease with two different PRNP variants

scientific article published on 17 January 2020

A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease

scientific article published on 19 June 2020

A young-onset frontal dementia with dramatic calcifications due to a novel CSF1R mutation

scientific article published on 19 April 2016

Aerophagia as the initial presenting symptom of a depressed patient

scientific article

Assessment of executive function declines in presymptomatic and mildly symptomatic familial frontotemporal dementia: NIH-EXAMINER as a potential clinical trial endpoint

scientific article published on 01 January 2020

Autoimmune-mediated cognitive impairment: a case report

scientific article

Caregiver burden in atypical dementias: comparing frontotemporal dementia, Creutzfeldt-Jakob disease, and Alzheimer's disease.

scientific article published on 5 October 2015

Characteristics of established and proposed sporadic Creutzfeldt-Jakob disease variants

scientific article published in February 2009

Chronic Wasting Disease in Cervids: Implications for Prion Transmission to Humans and Other Animal Species

scientific article published on 23 July 2019

Clinical Laboratory Tests Used To Aid in Diagnosis of Human Prion Disease

scientific article published on 24 September 2019

Clinical Use of Improved Diagnostic Testing for Detection of Prion Disease

scientific article

Clinical and imaging characteristics of late onset mitochondrial membrane protein-associated neurodegeneration (MPAN)

scientific article published on November 2016

Clinical and volumetric changes with increasing functional impairment in familial frontotemporal lobar degeneration

scientific article published on 06 January 2020

Clozapine for treatment-resistant agitation in dementia

scientific article published on September 2007

Co-occurrence of chronic traumatic encephalopathy and prion disease

Comprehensive and Methodical: Diagnostic and Management Approaches to Rapidly Progressive Dementia

scientific article published on 30 September 2017

Correction to: In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP Mutation

scientific article published on 01 August 2019

D178N, 129Val and N171S, 129Val Genotype in a Family with Creutzfeldt-Jakob Disease ⬇️

scientific article published on November 12, 2010

Diagnosis of Prion Diseases by RT-QuIC Results in Improved Surveillance

scientific article published on 22 June 2020

Diagnostic and prognostic value of human prion detection in cerebrospinal fluid

scientific article

Discovering new treatments for Alzheimer's disease by repurposing approved medications

scientific article

Distinct prion-like strains of amyloid beta implicated in phenotypic diversity of Alzheimer's disease

scientific article published on 25 January 2016

Does the presentation of Creutzfeldt-Jakob disease vary by age or presumed etiology? A meta-analysis of the past 10 years

scientific article published on January 2007

Early detection of periodic sharp wave complexes on EEG by independent component analysis in patients with Creutzfeldt-Jakob disease

scientific article published in August 2008

Early preclinical detection of prions in the skin of prion-infected animals

scientific article published in Nature Communications

Estimating severity of illness and disability in Frontotemporal Dementia: Preliminary analysis of the Dementia Disability Rating (DDR).

scientific article published on January 2011

Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging

scientific article published on 01 June 2020

Fatal familial insomnia and sporadic fatal insomnia

scientific article published on 01 January 2018

Feasibility of Remote Assessment of Human Prion Diseases for Research and Surveillance

scientific article published on 12 March 2019

Fluorodeoxyglucose Positron Emission Tomography (FDG-PET) Correlation of Histopathology and MRI in Prion Disease

scientific article

From Neurodegeneration to Brain Health: An Integrated Approach.

scientific article published on 26 February 2015

Genetic screening of a large series of North American sporadic and familial frontotemporal dementia cases

scientific article published on 01 January 2020

Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases

scientific article

Human Prion Disease Surveillance in Washington State, 2006-2017

scientific article published on 01 October 2020

Human prion diseases

scientific article published on 01 June 2019

Iatrogenic Creutzfeldt-Jakob disease from commercial cadaveric human growth hormone.

scientific article published in April 2013

Iatrogenic Creutzfeldt-Jakob disease with Amyloid-β pathology: an international study

scientific article published on 8 January 2018

Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study

scientific article published on 16 September 2020

Impaired transmissibility of atypical prions from genetic CJD

In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP Mutation

scientific article published on 05 January 2019

Individualized atrophy scores predict dementia onset in familial frontotemporal lobar degeneration

scientific article published on 06 January 2020

Initial diagnoses of patients ultimately diagnosed with prion disease

scientific article

Mania as a possible prodrome to dementia

scientific article published on 01 January 2007

Many challenges of conducting clinical trials in CJD.

scientific article published on 4 November 2016

Neuropsychiatric symptoms in MCI subtypes: the importance of executive dysfunction.

scientific article

Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type

scientific article published on 16 January 2017

PMCA-replicated PrPD in urine of vCJD patients maintains infectivity and strain characteristics of brain PrPD: Transmission study

article

Patient With voltage-gated potassium-channel (VGKC) limbic encephalitis found to have Creutzfeldt-Jakob disease (CJD) at autopsy

scientific article published in January 2013

Predictors of depression and anxiety in patients with intracranial neoplasms

scientific article published on January 2008

Prion disease incidence in the United States: 2003-2015

scientific article published on 22 November 2019

Prion diseases: targets and treatments of symptoms and disease progression. Editorial

scientific article published in November 2009

Prion propagation estimated from brain diffusion MRI is subtype dependent in sporadic Creutzfeldt-Jakob disease

scientific article published on 13 June 2020

Prion seeding activity and infectivity in skin samples from patients with sporadic Creutzfeldt-Jakob disease.

scientific article published in November 2017

Psychiatric and neuropsychiatric adverse events associated with deep brain stimulation: A meta-analysis of ten years' experience.

scientific article

Psychotropic medications and the treatment of human prion diseases

scientific article

Publisher Correction: Early preclinical detection of prions in the skin of prion-infected animals

scientific article published in Nature Communications

Racial and Ethnic Differences in Individuals with Sporadic Creutzfeldt-Jakob Disease in the United States of America ⬇️

scientific article published on June 18, 2012

Rapidly Progressive Alzheimer's Disease in Two Distinct Autopsy Cohorts.

scientific article published in January 2018

Rapidly progressive Alzheimer's disease features distinct structures of amyloid-β.

scientific article published on 15 February 2015

Rapidly progressive dementias and the treatment of human prion diseases ⬇️

scientific article published on November 23, 2010

Rapidly progressive young-onset dementias: neuropsychiatric aspects

scientific article published on 02 March 2015

Scientific and ethical issues related to deep brain stimulation for disorders of mood, behavior, and thought

scientific article

Severe hyponatremia and seizures secondary to psychogenic polydipsia in a case of frontotemporal dementia

scientific article

Shortening heparan sulfate chains prolongs survival and reduces parenchymal plaques in prion disease caused by mobile, ADAM10-cleaved prions

scientific article published on 31 October 2019

Should we be teaching philosophy to psychiatrists-in-training?

scientific article published on 01 May 2007

Sporadic Creutzfeldt-Jakob disease: changes not only in the brain?

scientific article published in August 2012

Streamlined alpha-synuclein RT-QuIC assay for various biospecimens in Parkinson's disease and dementia with Lewy bodies

scientific article

Subclavian steal syndrome presenting as a reversible dementia

scientific article published on 01 January 2015

Subtype diagnosis of sporadic Creutzfeldt-Jakob disease with diffusion MRI

scientific article published on 03 December 2020

Symptomatic treatment, care, and support of CJD patients

scientific article published on 01 January 2018

The Complexity of Deep Brain Stimulation and Suicidality in Patients with Treatment Resistant Depression

The association of neuropsychiatric symptoms in MCI with incident dementia and Alzheimer disease.

scientific article

Therapeutic strategies for prion disease: a practical perspective

scientific article published on 30 November 2018

Trace and transference: therapy in a post-structuralist era.

scientific article published in January 2008

Unusual Case of Sporadic Creutzfeldt-Jakob Disease Subtype VV1.

scientific article published in January 2015

Utility of the global CDR® plus NACC FTLD rating and development of scoring rules: Data from the ARTFL/LEFFTDS Consortium

scientific article published on 01 January 2020

Variably protease-sensitive prionopathy

scientific article published on 01 January 2018

Visual art therapy in sporadic Creutzfeldt-Jakob disease: a case study

scientific article published on 18 January 2016

List of works by Brian S Appleby

A Practical Primer on Prion Pathology

A Review: Treatment of Alzheimer’s Disease Discovered in Repurposed Agents ⬇️

A case report of genetic prion disease with two different PRNP variants

A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease

A young-onset frontal dementia with dramatic calcifications due to a novel CSF1R mutation

Aerophagia as the initial presenting symptom of a depressed patient

Assessment of executive function declines in presymptomatic and mildly symptomatic familial frontotemporal dementia: NIH-EXAMINER as a potential clinical trial endpoint

Autoimmune-mediated cognitive impairment: a case report

Caregiver burden in atypical dementias: comparing frontotemporal dementia, Creutzfeldt-Jakob disease, and Alzheimer's disease.

Characteristics of established and proposed sporadic Creutzfeldt-Jakob disease variants

Chronic Wasting Disease in Cervids: Implications for Prion Transmission to Humans and Other Animal Species

Clinical Laboratory Tests Used To Aid in Diagnosis of Human Prion Disease

Clinical Use of Improved Diagnostic Testing for Detection of Prion Disease

Clinical and imaging characteristics of late onset mitochondrial membrane protein-associated neurodegeneration (MPAN)

Clinical and volumetric changes with increasing functional impairment in familial frontotemporal lobar degeneration

Clozapine for treatment-resistant agitation in dementia

Co-occurrence of chronic traumatic encephalopathy and prion disease

Comprehensive and Methodical: Diagnostic and Management Approaches to Rapidly Progressive Dementia

Correction to: In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP Mutation

D178N, 129Val and N171S, 129Val Genotype in a Family with Creutzfeldt-Jakob Disease ⬇️

Diagnosis of Prion Diseases by RT-QuIC Results in Improved Surveillance

Diagnostic and prognostic value of human prion detection in cerebrospinal fluid

Discovering new treatments for Alzheimer's disease by repurposing approved medications

Distinct prion-like strains of amyloid beta implicated in phenotypic diversity of Alzheimer's disease

Does the presentation of Creutzfeldt-Jakob disease vary by age or presumed etiology? A meta-analysis of the past 10 years

Early detection of periodic sharp wave complexes on EEG by independent component analysis in patients with Creutzfeldt-Jakob disease

Early preclinical detection of prions in the skin of prion-infected animals

Estimating severity of illness and disability in Frontotemporal Dementia: Preliminary analysis of the Dementia Disability Rating (DDR).

Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging

Fatal familial insomnia and sporadic fatal insomnia

Feasibility of Remote Assessment of Human Prion Diseases for Research and Surveillance

Fluorodeoxyglucose Positron Emission Tomography (FDG-PET) Correlation of Histopathology and MRI in Prion Disease

From Neurodegeneration to Brain Health: An Integrated Approach.

Genetic screening of a large series of North American sporadic and familial frontotemporal dementia cases

Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases

Human Prion Disease Surveillance in Washington State, 2006-2017

Human prion diseases

Iatrogenic Creutzfeldt-Jakob disease from commercial cadaveric human growth hormone.

Iatrogenic Creutzfeldt-Jakob disease with Amyloid-β pathology: an international study

Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study

Impaired transmissibility of atypical prions from genetic CJD

In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP Mutation

Individualized atrophy scores predict dementia onset in familial frontotemporal lobar degeneration

Initial diagnoses of patients ultimately diagnosed with prion disease

Mania as a possible prodrome to dementia

Many challenges of conducting clinical trials in CJD.

Neuropsychiatric symptoms in MCI subtypes: the importance of executive dysfunction.

Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type

PMCA-replicated PrPD in urine of vCJD patients maintains infectivity and strain characteristics of brain PrPD: Transmission study

Patient With voltage-gated potassium-channel (VGKC) limbic encephalitis found to have Creutzfeldt-Jakob disease (CJD) at autopsy

Predictors of depression and anxiety in patients with intracranial neoplasms

Prion disease incidence in the United States: 2003-2015

Prion diseases: targets and treatments of symptoms and disease progression. Editorial

Prion propagation estimated from brain diffusion MRI is subtype dependent in sporadic Creutzfeldt-Jakob disease

Prion seeding activity and infectivity in skin samples from patients with sporadic Creutzfeldt-Jakob disease.

Psychiatric and neuropsychiatric adverse events associated with deep brain stimulation: A meta-analysis of ten years' experience.

Psychotropic medications and the treatment of human prion diseases

Publisher Correction: Early preclinical detection of prions in the skin of prion-infected animals

Racial and Ethnic Differences in Individuals with Sporadic Creutzfeldt-Jakob Disease in the United States of America ⬇️

Rapidly Progressive Alzheimer's Disease in Two Distinct Autopsy Cohorts.

Rapidly progressive Alzheimer's disease features distinct structures of amyloid-β.

Rapidly progressive dementias and the treatment of human prion diseases ⬇️

Rapidly progressive young-onset dementias: neuropsychiatric aspects

Scientific and ethical issues related to deep brain stimulation for disorders of mood, behavior, and thought

Severe hyponatremia and seizures secondary to psychogenic polydipsia in a case of frontotemporal dementia

Shortening heparan sulfate chains prolongs survival and reduces parenchymal plaques in prion disease caused by mobile, ADAM10-cleaved prions

Should we be teaching philosophy to psychiatrists-in-training?

Sporadic Creutzfeldt-Jakob disease: changes not only in the brain?

Streamlined alpha-synuclein RT-QuIC assay for various biospecimens in Parkinson's disease and dementia with Lewy bodies

Subclavian steal syndrome presenting as a reversible dementia

Subtype diagnosis of sporadic Creutzfeldt-Jakob disease with diffusion MRI

Symptomatic treatment, care, and support of CJD patients

The Complexity of Deep Brain Stimulation and Suicidality in Patients with Treatment Resistant Depression

The association of neuropsychiatric symptoms in MCI with incident dementia and Alzheimer disease.

Therapeutic strategies for prion disease: a practical perspective

Trace and transference: therapy in a post-structuralist era.

Unusual Case of Sporadic Creutzfeldt-Jakob Disease Subtype VV1.

Utility of the global CDR® plus NACC FTLD rating and development of scoring rules: Data from the ARTFL/LEFFTDS Consortium

Variably protease-sensitive prionopathy