Search filters

List of works by Richard J Dirven

Angiogenic characteristics of blood outgrowth endothelial cells from patients with von Willebrand disease

scientific article published on 21 September 2015

Biogenesis of Weibel-Palade bodies in von Willebrand's disease variants with impaired von Willebrand factor intrachain or interchain disulfide bond formation ⬇️

scientific article published on December 29, 2011

Characterization of an immunologic polymorphism (D79H) in the heavy chain of factor V.

scientific article

Correction of a dominant-negative von Willebrand factor multimerization defect by small interfering RNA-mediated allele-specific inhibition of mutant von Willebrand factor

scientific article published on 01 June 2018

Ex vivo Improvement of a von Willebrand Disease Type 2A Phenotype Using an Allele-Specific Small-Interfering RNA

scientific article published on 15 August 2020

Intracellular storage and regulated secretion of von Willebrand factor in quantitative von Willebrand disease

scientific article published on 19 May 2011

No evidence for a direct effect of von Willebrand factor's ABH blood group antigens on von Willebrand factor clearance.

scientific article

Storage and secretion of naturally occurring von Willebrand factor A domain variants

scientific article published on 08 August 2014

The R2-haplotype associated Asp2194Gly mutation in the light chain of human factor V results in lower expression levels of FV, but has no influence on the glycosylation of Asn2181.

scientific article published in March 2003

The R306G and R506Q mutations in coagulation Factor V reveals additional cleavage sites for Activated Protein C in the R313-R321 region and at R505.

scientific article published on 3 January 2010

The activated protein C (APC)-resistant phenotype of APC cleavage site mutants of recombinant factor V in a reconstituted plasma model.

scientific article

VWF propeptide and ratios between VWF, VWF propeptide, and FVIII in the characterization of type 1 von Willebrand disease ⬇️

scientific article published on January 24, 2013

Variability of von Willebrand factor-related parameters in endothelial colony forming cells

scientific article published on 22 July 2019

Paulina is supported by:

About Paulina

Help