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List of works by Ulrich Costabel

58-year old woman with primary biliary cirrhosis and crepitations

scientific article published in December 2015

6-Minute walk distance is an independent predictor of mortality in patients with idiopathic pulmonary fibrosis

scientific article published on 5 December 2013

A Comparison of Existing Questionnaires for Identifying the Causes of Interstitial and Rare Lung Diseases

scientific article published on 30 January 2020

A Global Survey on Whole Lung Lavage in Pulmonary Alveolar Proteinosis

scientific article published in July 2016

A female soccer player with recurrent haemoptysis and iron deficiency anaemia: idiopathic pulmonary haemosiderosis (IPH)--case report and literature review ⬇️

scientific article published on January 13, 2010

A pilot study: a combined therapy using polymyxin-B hemoperfusion and extracorporeal membrane oxygenation for acute exacerbation of interstitial pneumonia

scientific article published on 5 January 2015

All-cause mortality rate in patients with idiopathic pulmonary fibrosis. Implications for the design and execution of clinical trials.

scientific article published in April 2014

Alveolar extracellular 20S proteasome in patients with acute respiratory distress syndrome

scientific article published on 12 March 2009

An Important Step Forward, but Still a Way to Go

article by Wim A. Wuyts et al published February 2016 in American Journal of Respiratory and Critical Care Medicine

An Open-Label Study of the Long-Term Safety of Pirfenidone in Patients with Idiopathic Pulmonary Fibrosis (RECAP).

scientific article published on 13 September 2017

An emerging frontier in the treatment of acute exacerbation of idiopathic pulmonary fibrosis

scientific article published on 27 December 2017

An official ATS/ERS/JRS/ALAT statement: idiopathic pulmonary fibrosis: evidence-based guidelines for diagnosis and management

scientific article

An official American Thoracic Society clinical practice guideline: the clinical utility of bronchoalveolar lavage cellular analysis in interstitial lung disease

scientific article published on May 2012

An official American Thoracic Society/European Respiratory Society statement: Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias

scientific article

Analysis of lung function and survival in RECAP: An open-label extension study of pirfenidone in patients with idiopathic pulmonary fibrosis.

scientific article published on 20 October 2014

Angiogenic and angiostatic chemokines in idiopathic pulmonary fibrosis and granulomatous lung disease

scientific article published on 06 October 2009

Antacid Therapy and Disease Progression in Patients with Idiopathic Pulmonary Fibrosis Who Received Pirfenidone.

scientific article

Antacid therapy and disease outcomes in idiopathic pulmonary fibrosis: a pooled analysis.

scientific article

Anti-acid therapy in idiopathic pulmonary fibrosis: insights from the INPULSIS® trials

Anti-acid treatment in patients with IPF: interpret results from post-hoc, subgroup, and exploratory analyses with great caution - Authors' reply.

scientific article published in September 2016

Ascertainment of individual risk of mortality for patients with idiopathic pulmonary fibrosis

scientific article

Baseline High-Resolution CT Findings Predict Acute Exacerbation of Idiopathic Pulmonary Fibrosis: German and Japanese Cohort Study

scientific article published on 24 November 2019

Baseline KL-6 predicts increased risk for acute exacerbation of idiopathic pulmonary fibrosis

scientific article published on 26 April 2014

Biomarkers in connective tissue disease-associated interstitial lung disease

scientific article published on 25 March 2014

Bronchiolar disorders: classification and diagnostic approach

scientific article

Bronchoalveolar lavage in drug-induced lung disease

scientific article published on March 2004

Bronchoalveolar lavage in other interstitial lung diseases

scientific article

Bronchoscopic Lung Cryobiopsy Increases Diagnostic Confidence in the Multidisciplinary Diagnosis of Idiopathic Pulmonary Fibrosis.

scientific article

CC-chemokine ligand 2 inhibition in idiopathic pulmonary fibrosis: a phase 2 trial of carlumab

scientific article published on 22 October 2015

CCL18 in serum, BAL fluid and alveolar macrophage culture supernatant in interstitial lung diseases ⬇️

scientific article published on July 5, 2013

CD4+CD25+ T-cell populations expressing CD134 and GITR are associated with disease activity in patients with Wegener's granulomatosis

scientific article published on 22 August 2008

Challenges in IPF diagnosis, current management and future perspectives

scientific article published on 03 August 2015

Changes in chest roentgenogram of sarcoidosis patients during a clinical trial of infliximab therapy: comparison of different methods of evaluation.

scientific article published on 24 April 2009

Chronic Hypersensitivity Pneumonitis ⬇️

scientific article published on January 24, 2012

Classification of hypersensitivity pneumonitis: a hypothesis

scientific article published on 6 January 2009

Clinical Manifestations of Respiratory Bronchiolitis as an Incidental Finding in Surgical Lung Biopsies: A Retrospective Analysis of a Large Austrian Registry

scientific article

Clinical diagnosis of hypersensitivity pneumonitis

scientific article published on 3 July 2003

Clinical features of recurrent and insidious chronic bird fancier's lung

scientific article

Clinical presentation, outcome and risk factors of late-onset non-infectious pulmonary complications after allogeneic stem cell transplantation

scientific article published on May 2009

Cockade-like structures in alveolar macrophages in extrinsic allergic alveolitis

scientific article published in January 2005

Colpoplasty and acute pneumonitis

scientific article published in January 2003

Combination therapy: the future of management for idiopathic pulmonary fibrosis?

scientific article

Comparison of serum KL-6 versus bronchoalveolar lavage neutrophilia for the diagnosis of bronchiolitis obliterans in lung transplantation

scientific article published on 25 August 2011

Comprehensive assessment of the long-term safety of pirfenidone in patients with idiopathic pulmonary fibrosis

scientific article

Delphi consensus recommendations for a treatment algorithm in pulmonary sarcoidosis

scientific article published on 20 March 2020

Diagnosis of Sarcoidosis

scientific article published in August 2015

Diagnosis of sarcoidosis

scientific article published on 01 September 2008

Diagnostic approach to interstitial pneumonias in a single centre: report on 88 cases ⬇️

scientific article published on November 26, 2012

Diagnostic modalities in sarcoidosis: BAL, EBUS, and PET

scientific article published on 27 July 2010

Diagnostic value of BAL lymphocytosis in patients with indeterminate for usual interstitial pneumonia imaging pattern

scientific article published on 14 November 2019

Differences in serum SP-D levels between German and Japanese subjects are associated with SFTPD gene polymorphisms

scientific article published on 08 January 2014

Different MUC1 gene polymorphisms in German and Japanese ethnicities affect serum KL-6 levels

scientific article

Differential diagnosis of granulomatous lung disease: clues and pitfalls: Number 4 in the Series "Pathology for the clinician" Edited by Peter Dorfmüller and Alberto Cavazza

scientific article published on 9 August 2017

Drug-induced respiratory disease in patients with hematological diseases

scientific article

EBUS-TBNA for the diagnosis of sarcoidosis: is it the only game in town?

scientific article

Effect of continued treatment with pirfenidone following clinically meaningful declines in forced vital capacity: analysis of data from three phase 3 trials in patients with idiopathic pulmonary fibrosis

scientific article

Effect of interferon gamma-1b on survival in patients with idiopathic pulmonary fibrosis (INSPIRE): a multicentre, randomised, placebo-controlled trial

scientific article

Effect of pirfenidone in patients with more advanced idiopathic pulmonary fibrosis

article published in 2019

Effect of pirfenidone on mortality: pooled analyses and meta-analyses of clinical trials in idiopathic pulmonary fibrosis.

scientific article published on 18 November 2016

Effect of statins on disease-related outcomes in patients with idiopathic pulmonary fibrosis

scientific article published on 05 October 2016

Efficacy and safety of nintedanib in idiopathic pulmonary fibrosis

scientific article (publication date: 29 May 2014)

Efficacy of Nintedanib in Idiopathic Pulmonary Fibrosis across Prespecified Subgroups in INPULSIS.

scientific article published on 22 September 2015

Efficacy of Pirfenidone in the Context of Multiple Disease Progression Events in Patients With Idiopathic Pulmonary Fibrosis

scientific article published on 22 November 2018

Efficacy of a tyrosine kinase inhibitor in idiopathic pulmonary fibrosis

scientific article

Efficacy of pirfenidone in patients with idiopathic pulmonary fibrosis with more preserved lung function

scientific article published on 28 July 2016

Erratum to: Pirfenidone in Idiopathic Pulmonary Fibrosis: Expert Panel Discussion on the Management of Drug-Related Adverse Events.

scientific article published on 8 May 2014

Extrinsic allergic alveolitis: inhibitory effects of pentoxifylline on cytokine production by alveolar macrophages

scientific article published in February 2004

FAM13A polymorphism as a prognostic factor in patients with idiopathic pulmonary fibrosis

scientific article published on 22 December 2016

Forced Vital Capacity in Patients with Idiopathic Pulmonary Fibrosis ⬇️

article by Roland M. du Bois et al published 15 December 2011 in American Journal of Respiratory and Critical Care Medicine

Gastroesophageal Reflux Disease in Idiopathic Pulmonary Fibrosis: Uncertainties and Controversies

scientific article published on 11 October 2018

German Guideline for Idiopathic Pulmonary Fibrosis - Update on Pharmacological Therapies 2017

scientific article published on 5 July 2017

German Guideline for Idiopathic Pulmonary Fibrosis - Update on Pharmacological Therapies 2017

scientific article

German Guideline for Idiopathic Pulmonary Fibrosis - Update on Pharmacological Therapies 2017.

scientific article

High-dose acetylcysteine in idiopathic pulmonary fibrosis

scientific article

Hot of the breath: Mortality as a primary end-point in IPF treatment trials: the best is the enemy of the good

How to handle IPF--the new Portuguese consensus document

scientific article published on 01 March 2016

Hypersensitivity pneumonitis

scientific article published on 13 September 2012

Idiopathic bronchiolitis mimicking diffuse panbronchiolitis.

scientific article published in March 2003

Idiopathic interstitial pneumonia or idiopathic interstitial pneumonitis: what's in a name?

scientific article published on 14 February 2019

Idiopathic pulmonary fibrosis in 2011: key updates on guidelines and therapeutics Concluding remarks ⬇️

scientific article published on April 16, 2013

Idiopathic pulmonary fibrosis: recent milestones in disease management ⬇️

scientific article published on 01 June 2012

Immune cells in bronchoalveolar lavage in peripheral lung cancer--analysis of 140 cases

scientific article published in January 2003

Increased expression of tumor necrosis factor receptors in cryptogenic organizing pneumonia ⬇️

scientific article published on 08 December 2010

Inflammatory profile and response to anti-tumor necrosis factor therapy in patients with chronic pulmonary sarcoidosis

scientific article

Infliximab for chronic cutaneous sarcoidosis: a subset analysis from a double-blind randomized clinical trial

Infliximab therapy in patients with chronic sarcoidosis and pulmonary involvement

scientific article

Inhibition of cytokine release from alveolar macrophages in pulmonary sarcoidosis by pentoxifylline

scientific article published in July 2003

Inhibition of cytokine release from alveolar macrophages in pulmonary sarcoidosis by pentoxifylline: comparison with dexamethasone

scientific article published in October 2003

Interleukin 12, interleukin 18, and tumor necrosis factor alpha release by alveolar macrophages: acute and chronic hypersensitivity pneumonitis

scientific article published in February 2009

Interstitial lung disease.

scientific article

Interstitial pneumonia with autoimmune features: a critical appraisal of the new definition

scientific article published on July 2016

KL-6, a Human MUC1 Mucin, as a prognostic marker for diffuse alveolar hemorrhage syndrome

scientific article published on 17 December 2012

Localization of Propionibacterium acnes in granulomas supports a possible etiologic link between sarcoidosis and the bacterium ⬇️

scientific article published on May 18, 2012

Long-term safety and tolerability of nintedanib in patients with idiopathic pulmonary fibrosis: results from the open-label extension study, INPULSIS-ON

scientific article published on 14 September 2018

Long-term treatment of patients with idiopathic pulmonary fibrosis with nintedanib: results from the TOMORROW trial and its open-label extension

scientific article

Lung function in idiopathic pulmonary fibrosis--extended analyses of the IFIGENIA trial

scientific article published on 27 October 2009

MFAP4: a candidate biomarker for hepatic and pulmonary fibrosis?

MUC1 gene polymorphisms are associated with serum KL-6 levels and pulmonary dysfunction in pulmonary alveolar proteinosis

scientific article published on 23 April 2016

MUC5B promoter polymorphism in Japanese patients with idiopathic pulmonary fibrosis

scientific article published on 08 January 2015

Macrolides inhibit cytokine production by alveolar macrophages in bronchiolitis obliterans organizing pneumonia ⬇️

scientific article published on 02 November 2012

Pamrevlumab, an anti-connective tissue growth factor therapy, for idiopathic pulmonary fibrosis (PRAISE): a phase 2, randomised, double-blind, placebo-controlled trial

scientific article published on 28 September 2019

Phenotypes of organ involvement in sarcoidosis

scientific article published on 25 January 2018

Pirfenidone for idiopathic pulmonary fibrosis: analysis of pooled data from three multinational phase 3 trials

scientific article

Pirfenidone in idiopathic pulmonary fibrosis: expert panel discussion on the management of drug-related adverse events

scientific article

Pirfenidone in patients with idiopathic pulmonary fibrosis (CAPACITY): two randomised trials ⬇️

scientific article (publication date: 21 May 2011)

Pirfenidone in patients with idiopathic pulmonary fibrosis and more advanced lung function impairment

scientific article published on 24 April 2019

Pirfenidone safety and adverse event management in idiopathic pulmonary fibrosis

scientific article published on 6 December 2017

Preliminary study on effect of pentoxifylline in treatment of extrinsic allergic alveolitis

scientific article published in March 2004

Production of IL-12, IL-18 and TNF-alpha by alveolar macrophages in hypersensitivity pneumonitis

scientific article published on 01 October 2004

Production of soluble tumor necrosis factor receptors and tumor necrosis factor-alpha by alveolar macrophages in sarcoidosis and extrinsic allergic alveolitis

scientific article published on 01 January 2005

Prof. Om Prakash Sharma, 1936–2012 ⬇️

scientific article published on November 1, 2012

Pulmonary Complications of Hematological Disorders

Pulmonary alveolar proteinosis associated with dust inhalation: not secondary but autoimmune?

scientific article published on 01 March 2010

Pulmonary alveolar proteinosis: New insights from a single-center cohort of 70 patients ⬇️

scientific article published on September 6, 2011

Pulmonary alveolar proteinosis: a new autoimmune disease.

scientific article

Pulmonary alveolar proteinosis: another autoimmune disease associated with sarcoidosis?

scientific article published on 29 March 2016

Pulmonary complications in patients with hematological disorders: pathobiological bases and practical approach

scientific article

Quantitative Analysis of Mycobacterial and Propionibacterial DNA in Lymph Nodes of Japanese and European Patients with Sarcoidosis ⬇️

scientific article published on January 1, 2002

Quantitative Lipidomics in Pulmonary Alveolar Proteinosis

scientific article published on 01 October 2019

Rare infiltrative lung diseases: a challenge for clinicians

scientific article published in September 2004

Reactive alveolar epithelium in chondroid hamartoma of the lung

scientific article published in March 2005

Reply: Effect of Nintedanib in Patients with Idiopathic Pulmonary Fibrosis

scientific article published in May 2017

Safety and efficacy of ustekinumab or golimumab in patients with chronic sarcoidosis

scientific article published on 17 July 2014

Safety of pirfenidone in patients with idiopathic pulmonary fibrosis: integrated analysis of cumulative data from 5 clinical trials

scientific article

Sarcoidosis

scientific article published on 27 July 2010

Sarcoidosis in America. Analysis Based on Health Care Use.

scientific article

Serum KL-6 is a predictor of outcome in pulmonary alveolar proteinosis ⬇️

scientific article published on April 4, 2013

Serum YKL-40 as predictor of outcome in hypersensitivity pneumonitis

scientific article published on 11 November 2016

Serum YKL-40 in workers at an indium-tin oxide production facility - Reply

scientific article

Serum YKL-40 is a reliable biomarker for pulmonary alveolar proteinosis

scientific article published on 31 May 2017

Significance of bronchoalveolar lavage for the diagnosis of idiopathic pulmonary fibrosis

scientific article published on 26 February 2009

Six-minute-walk test in idiopathic pulmonary fibrosis: test validation and minimal clinically important difference

scientific article

Smoking-related idiopathic interstitial pneumonia

scientific article

Statin Therapy and Outcomes in Trials of Nintedanib in Idiopathic Pulmonary Fibrosis.

scientific article published on 7 February 2018

Suggestions for improving clinical utility of future guidelines for diagnosis and management of IPF - results of a Delphi survey

scientific article published on 08 January 2021

Surfactant protein A detection in large cell carcinoma of the lung

scientific article published on 01 March 2006

Surfactant protein A detection in primary pulmonary adenocarcinoma without bronchioloalveolar pattern

scientific article published in May 2005

Systemic evaluation of a potential cutaneous sarcoidosis patient

scientific article published on May 2007

The European IPF registry (eurIPFreg): baseline characteristics and survival of patients with idiopathic pulmonary fibrosis

The European Respiratory Society spirometry tent: a unique form of screening for airway obstruction

scientific article published on 20 January 2012

The International LAM Registry: a component of an innovative web-based clinician, researcher, and patient-driven rare disease research platform.

scientific article published on March 2010

The WASOG Sarcoidosis Organ Assessment Instrument: An update of a previous clinical tool

The changing treatment landscape in idiopathic pulmonary fibrosis

scientific article published on March 2015

The potential additional benefit of infliximab in patients with chronic pulmonary sarcoidosis already receiving corticosteroids: a retrospective analysis from a randomized clinical trial

scientific article

Transbronchial Lung Cryobiopsy in Diffuse Parenchymal Lung Disease: Comparison between Biopsy from 1 Segment and Biopsy from 2 Segments - Diagnostic Yield and Complications

scientific article published in March 2017

Treatment of idiopathic pulmonary fibrosis with ambrisentan: a parallel, randomized trial

scientific article

Treatment of idiopathic pulmonary fibrosis with etanercept: an exploratory, placebo-controlled trial

scientific article published on 31 July 2008

Treatment of sarcoidosis

scientific article published on 01 September 2008

Unfavourable effects of medically indicated oral anticoagulants on survival in idiopathic pulmonary fibrosis: methodological concerns

scientific article published on 01 November 2016

Utility of Anti-DSF70 Antibodies to Predict Connective Tissue Disease in Patients Originally Presenting with Idiopathic Interstitial Pneumonia

scientific article published on 29 March 2019

Validation of test performance characteristics and minimal clinically important difference of the 6-minute walk test in patients with idiopathic pulmonary fibrosis

scientific article published on 24 April 2015

Wash-out kinetics and efficacy of a modified lavage technique for alveolar proteinosis ⬇️

scientific article published on April 10, 2012

When the game changes: Guidance to adjust sarcoidosis management during the COVID-19 pandemic

scientific article published on 29 April 2020

Whole lung lavage therapy for pulmonary alveolar proteinosis: a global survey of current practices and procedures.

scientific article published on 31 August 2016

[58-year old woman with primary biliary cirrhosis and crepitations]

scientific article published on 17 February 2016

[Current trends in pneumology 2002 -- Part 1]

scientific article published on 01 January 2003

[DGP Newsletter September 2009]

scientific article published on 11 September 2009

[Reply]

scientific article published on 07 June 2013

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