List of works - Joanna Pepke-Zaba

(18)FDG PET imaging can quantify increased cellular metabolism in pulmonary arterial hypertension: A proof-of-principle study

scientific article published in October 2011

A multicenter study of anticoagulation in operable chronic thromboembolic pulmonary hypertension

scientific article published on 18 October 2019

Age should not be a barrier for pulmonary endarterectomy in carefully selected patients

scientific article published on 7 December 2017

Anticoagulation and survival in pulmonary arterial hypertension: results from the Comparative, Prospective Registry of Newly Initiated Therapies for Pulmonary Hypertension (COMPERA).

scientific article published on 30 September 2013

Assessment of a pulmonary origin for blood outgrowth endothelial cells by examination of identical twins harboring a BMPR2 mutation

scientific article published in July 2013

Author's reply

BMPR-II mutations promote pulmonary arterial hypertension via a hyperinflammatory response

scientific article published on 29 May 2015

Balloon pulmonary angioplasty for inoperable chronic thromboembolic pulmonary hypertension: the UK experience

scientific article published on 27 February 2020

Bayesian Inference Associates Rare <i>KDR</i> Variants with Specific Phenotypes in Pulmonary Arterial Hypertension

scientific article published on 15 December 2020

Better off blue: BMPR-2 mutation, arteriovenous malformation, and pulmonary arterial hypertension

scientific article published in June 2014

Bone morphogenetic protein receptor type II deficiency and increased inflammatory cytokine production. A gateway to pulmonary arterial hypertension

scientific article

Bosentan for treatment of inoperable chronic thromboembolic pulmonary hypertension: BENEFiT (Bosentan Effects in iNopErable Forms of chronIc Thromboembolic pulmonary hypertension), a randomized, placebo-controlled trial

scientific article

CAMPHOR score: patient-reported outcomes are improved by pulmonary endarterectomy in chronic thromboembolic pulmonary hypertension (CTEPH)

scientific article published on 08 June 2020

COVID-19 in pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension: a reference centre survey

scientific article published on 01 October 2020

Cardiopulmonary exercise testing suggests a beneficial response to pulmonary endarterectomy in a patient with chronic thromboembolic obstruction and normal preoperative pulmonary hemodynamics

scientific article published on March 2014

Changing demographics, epidemiology, and survival of incident pulmonary arterial hypertension: results from the pulmonary hypertension registry of the United Kingdom and Ireland.

scientific article published on 12 July 2012

Characterization of GDF2 Mutations and Levels of BMP9 and BMP10 in Pulmonary Arterial Hypertension

scientific article published on 01 March 2020

Chronic Thromboembolic Pulmonary Hypertension. The Journey from a Curiosity to a Cure

scientific article published on July 2016

Chronic thromboembolic pulmonary hypertension (CTEPH): results from an international prospective registry

scientific article published on 3 October 2011

Chronic thromboembolic pulmonary hypertension: advances from bench to patient management

scientific article published on 01 January 2013

Chronic thromboembolic pulmonary hypertension: role of medical therapy

scientific article

Chronic thromboembolic pulmonary hypertension: time for research in pathophysiology to catch up with developments in treatment

scientific article

Connective Tissue Disease–associated Pulmonary Arterial Hypertension in the Modern Treatment Era

scientific article published on 17 October 2008

Current understanding of the role of bosentan in inoperable chronic thromboembolic pulmonary hypertension

scientific article

Decreased time constant of the pulmonary circulation in chronic thromboembolic pulmonary hypertension

scientific article published on 17 May 2013

Demographic features, BMPR2 status and outcomes in distal chronic thromboembolic pulmonary hypertension

scientific article

Demographics, clinical characteristics, health resource utilization and cost of chronic thromboembolic pulmonary hypertension patients: retrospective results from six European countries.

scientific article

Determinants of diagnostic delay in Chronic Thromboembolic Pulmonary Hypertension: results from the European CTEPH registry

scientific article published on 06 December 2018

Developments in pulmonary arterial hypertension-targeted therapy for chronic thromboembolic pulmonary hypertension

scientific article published on October 2015

Diagnosis, assessment, and treatment of non-pulmonary arterial hypertension pulmonary hypertension

scientific article

Dual-energy CT angiography for assessment of regional pulmonary perfusion in patients with chronic thromboembolic pulmonary hypertension: initial experience

scientific article

Dynamic Risk Stratification of Patient Long-Term Outcome After Pulmonary Endarterectomy: Results From the United Kingdom National Cohort

scientific article published on 6 April 2016

ERS Statement on Chronic Thromboembolic Pulmonary Hypertension

scientific article published on 17 December 2020

ERS statement on exercise training and rehabilitation in patients with severe chronic pulmonary hypertension

scientific article published on 28 February 2019

EXPRESS: Acute and chronic dissection of pulmonary artery: new challenges in pulmonary arterial hypertension?

scientific article published in January 2017

Elevated Levels of Inflammatory Cytokines Predict Survival in Idiopathic and Familial Pulmonary Arterial Hypertension

scientific article published on 16 August 2010

EmPHasis-10 health-related quality of life score predicts outcomes in patients with idiopathic and connective tissue disease-associated pulmonary arterial hypertension: results from a UK multi-centre study

scientific article published on 06 July 2020

Endothelin ETA receptors predominate in chronic thromboembolic pulmonary hypertension

scientific article published on 10 February 2016

Evidence of dysfunction of endothelial progenitors in pulmonary arterial hypertension

scientific article published on 23 July 2009

Exercise physiological responses to drug treatments in chronic thromboembolic pulmonary hypertension

scientific article published on 14 July 2016

Functional and haemodynamic outcome 1 year after pulmonary thromboendarterectomy

scientific article published on 22 May 2008

Genetic determinants of risk and survival in pulmonary arterial hypertension

article

Genetic determinants of risk in pulmonary arterial hypertension: international genome-wide association studies and meta-analysis

scientific article published on 05 December 2018

Guidelines on diagnosis and treatment of pulmonary arterial hypertension. The Task Force on Diagnosis and Treatment of Pulmonary Arterial Hypertension of the European Society of Cardiology

scientific article published on 01 December 2004

Identification of novel rare sequence variation underlying heritable pulmonary arterial hypertension

Identification of rare sequence variation underlying heritable pulmonary arterial hypertension.

scientific article published on 12 April 2018

Idiopathic pulmonary arterial hypertension and co-existing lung disease: is this a new phenotype?

scientific article published on 01 January 2020

Impaired Natural Killer Cell Phenotype and Function in Idiopathic and Heritable Pulmonary Arterial Hypertension

article

Improved Outcomes in Medically and Surgically Treated Chronic Thromboembolic Pulmonary Hypertension

scientific article published on 21 February 2008

Inefficient exercise gas exchange identifies pulmonary hypertension in chronic thromboembolic obstruction following pulmonary embolism

scientific article published on 27 September 2013

Interventional and surgical modalities of treatment for pulmonary arterial hypertension

scientific article published on June 2004

Interventional and surgical modalities of treatment in pulmonary hypertension

scientific article published on June 2009

Intravenous epoprostenol versus high dose inhaled iloprost for long-term treatment of pulmonary hypertension

scientific article published on 25 June 2010

Isolated large vessel pulmonary vasculitis as a cause of chronic obstruction of the pulmonary arteries

scientific article published on July 2011

Lifting the fog in intermediate-risk (submassive) PE: full dose, low dose, or no thrombolysis?

Limitations of resting haemodynamics in chronic thromboembolic disease without pulmonary hypertension

scientific article published on 17 January 2019

Log-transformation improves the prognostic value of serial NT-proBNP levels in apparently stable pulmonary arterial hypertension

scientific article

Long-Term Outcome of Patients With Chronic Thromboembolic Pulmonary Hypertension: Results From an International Prospective Registry.

scientific article published on 29 January 2016

Long-term use of sildenafil in inoperable chronic thromboembolic pulmonary hypertension

scientific article

Loss-of-Function ABCC8 Mutations in Pulmonary Arterial Hypertension

scientific article published on 01 October 2018

Maximal cardiac output determines 6 minutes walking distance in pulmonary hypertension

scientific article

Medical Therapy in Chronic Thromboembolic Pulmonary Hypertension

scientific article published on July 2016

Medical management of chronic thromboembolic pulmonary hypertension.

scientific article published on 29 March 2017

Medical therapies for chronic thromboembolic pulmonary hypertension: an evolving treatment paradigm

scientific article published on September 2006

Medication and patient factors associated with adherence to pulmonary hypertension targeted therapies

scientific article published in January 2017

Neutrophil Extracellular Traps Promote Angiogenesis: Evidence From Vascular Pathology in Pulmonary Hypertension.

scientific article published on 28 July 2016

Nitric oxide pathway and phosphodiesterase inhibitors in pulmonary arterial hypertension.

scientific article published on June 2004

Occlusion pressure analysis role in partitioning of pulmonary vascular resistance in CTEPH

scientific article published on 23 February 2012

Outcome after cardiopulmonary resuscitation in patients with pulmonary arterial hypertension.

scientific article published in February 2002

Outcome of pulmonary endarterectomy in symptomatic chronic thromboembolic disease

scientific article

Patient-reported outcomes assessed by the CAMPHOR questionnaire predict clinical deterioration in idiopathic pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension

scientific article

Phenotypic Characterization of EIF2AK4 Mutation Carriers in a Large Cohort of Patients Diagnosed Clinically With Pulmonary Arterial Hypertension

scientific article published on 28 September 2017

Plasma Metabolomics Implicates Modified Transfer RNAs and Altered Bioenergetics in the Outcomes of Pulmonary Arterial Hypertension.

scientific article

Plasma metabolomics exhibit response to therapy in chronic thromboembolic pulmonary hypertension

scientific article published on 15 October 2020

Pre-Capillary, Combined, and Post-Capillary Pulmonary Hypertension: A Pathophysiological Continuum

scientific article published on July 2016

Predicting survival in pulmonary arterial hypertension in the UK.

scientific article published on 3 May 2012

Presentation and management of pulmonary artery sarcoma

scientific article

Pulmonary arterial hypertension

scientific article published on 01 May 2010

Pulmonary arterial hypertension: epidemiology and registries

scientific article published on December 2013

Pulmonary arterial hypertension: epidemiology and registries

scientific article published in October 2014

Pulmonary arterial size and response to sildenafil in chronic thromboembolic pulmonary hypertension

scientific article

Pulmonary endarterectomy is effective and safe in patients with haemoglobinopathies and abnormal red blood cells: the Papworth experience

scientific article published on 17 March 2016

Pulmonary endarterectomy is possible and effective without the use of complete circulatory arrest--the UK experience in over 150 patients

scientific article published on February 2008

Pulmonary endarterectomy: outcomes in patients aged >70.

scientific article published on June 2012

Pulmonary hypertension in chronic lung disease and hypoxia

Pulmonary hypertension, nitric oxide and nitric oxide-releasing compounds

scientific article published on April 2011

Quality of life in patients with chronic thromboembolic pulmonary hypertension

scientific article

Reduced circulating BMP10 and BMP9 and elevated endoglin are associated with disease severity, decompensation and pulmonary vascular syndromes in patients with cirrhosis

scientific article published on 23 May 2020

Reply to "Letter to the editor: 'Pulsatile pulmonary artery pressure: are fluid-filled catheters accurate in pulmonary hypertension?'".

scientific article published on December 2013

Response by Cannon and Pepke-Zaba to Letter Regarding Article, "Dynamic Risk Stratification of Patient Long-Term Outcome After Pulmonary Endarterectomy: Results From the United Kingdom National Cohort"

scientific article published on 01 October 2016

Response to letters regarding article, "Anticoagulation and survival in pulmonary arterial hypertension: results from the Comparative, Prospective Registry of Newly Initiated Therapies for Pulmonary Hypertension (COMPERA)".

scientific article published in September 2014

Right ventricle functional assessment: have new techniques supplanted the old faithful conductance catheter?

scientific article published on September 2014

Right ventricular dysfunction in chronic thromboembolic obstruction of the pulmonary artery: a pressure-volume study using the conductance catheter

scientific article published on 19 December 2013

Right ventricular reverse remodeling after pulmonary endarterectomy: magnetic resonance imaging and clinical and right heart catheterization assessment

scientific article

Riociguat for pulmonary hypertension

scientific article published on 03 March 2014

Riociguat in patients with chronic thromboembolic pulmonary hypertension: results from an early access study

scientific article published on 28 December 2017

Risk assessment in medically treated chronic thromboembolic pulmonary hypertension patients

scientific article published on 08 November 2018

Risk of potentially life-threatening thyroid dysfunction due to amiodarone in idiopathic pulmonary arterial hypertension patients

scientific article published in February 2011

Role of NT-proBNP and 6MWD in chronic thromboembolic pulmonary hypertension

scientific article published on 13 August 2007

Serum osteoprotegerin is increased and predicts survival in idiopathic pulmonary arterial hypertension

scientific article published in January 2012

Sex-specific differences in chronic thromboembolic pulmonary hypertension. Results from the European CTEPH registry

scientific article published on 24 September 2019

Sildenafil improves health-related quality of life in patients with pulmonary arterial hypertension

scientific article published on January 2008

Supplementation of iron in pulmonary hypertension: Rationale and design of a phase II clinical trial in idiopathic pulmonary arterial hypertension

scientific article published on January 2013

Surgical management and outcome of patients with chronic thromboembolic pulmonary hypertension: results from an international prospective registry.

scientific article published in March 2011

Surgical treatment of pulmonary artery sarcoma

scientific article published on 01 June 2006

Survival after pulmonary thromboendarterectomy: effect of residual pulmonary hypertension

scientific article published on 13 May 2010

Survival in portopulmonary hypertension: Outcomes of the United Kingdom National Pulmonary Arterial Hypertension Registry.

scientific article published on 31 December 2016

Survival in pulmonary hypertension registries: the importance of incident cases

scientific article published on 01 June 2011

Tadalafil therapy and health-related quality of life in pulmonary arterial hypertension

scientific article published in October 2009

The ADAMTS13-VWF axis is dysregulated in chronic thromboembolic pulmonary hypertension

scientific article published on 28 March 2019

The CRASH report: emergency management dilemmas facing acute physicians in patients with pulmonary arterial hypertension.

scientific article published on 12 September 2017

The impact of patient choice on survival in chronic thromboembolic pulmonary hypertension

scientific article published on 16 September 2018

The outcome of reoperative pulmonary endarterectomy surgery

scientific article published on 23 January 2018

The potential effects of pregnancy in a patient with idiopathic pulmonary arterial hypertension responding to calcium channel blockade

scientific article

The resistance-compliance product of the pulmonary circulation varies in health and pulmonary vascular disease

scientific article

Traffic exposures, air pollution and outcomes in pulmonary arterial hypertension: A United Kingdom cohort study analysis

scientific article published on 30 May 2019

Unexplained iron deficiency in idiopathic and heritable pulmonary arterial hypertension

scientific article published on 05 February 2011

Ventriculo-arterial coupling detects occult RV dysfunction in chronic thromboembolic pulmonary vascular disease.

scientific article published on April 2017

Whole Blood RNA Profiles Associated with Pulmonary Arterial Hypertension and Clinical Outcome

scientific article published on 30 April 2020

List of works by Joanna Pepke-Zaba

(18)FDG PET imaging can quantify increased cellular metabolism in pulmonary arterial hypertension: A proof-of-principle study

A multicenter study of anticoagulation in operable chronic thromboembolic pulmonary hypertension

Age should not be a barrier for pulmonary endarterectomy in carefully selected patients

Anticoagulation and survival in pulmonary arterial hypertension: results from the Comparative, Prospective Registry of Newly Initiated Therapies for Pulmonary Hypertension (COMPERA).

Assessment of a pulmonary origin for blood outgrowth endothelial cells by examination of identical twins harboring a BMPR2 mutation

Author's reply

BMPR-II mutations promote pulmonary arterial hypertension via a hyperinflammatory response

Balloon pulmonary angioplasty for inoperable chronic thromboembolic pulmonary hypertension: the UK experience

Bayesian Inference Associates Rare <i>KDR</i> Variants with Specific Phenotypes in Pulmonary Arterial Hypertension

Better off blue: BMPR-2 mutation, arteriovenous malformation, and pulmonary arterial hypertension

Bone morphogenetic protein receptor type II deficiency and increased inflammatory cytokine production. A gateway to pulmonary arterial hypertension

Bosentan for treatment of inoperable chronic thromboembolic pulmonary hypertension: BENEFiT (Bosentan Effects in iNopErable Forms of chronIc Thromboembolic pulmonary hypertension), a randomized, placebo-controlled trial

CAMPHOR score: patient-reported outcomes are improved by pulmonary endarterectomy in chronic thromboembolic pulmonary hypertension (CTEPH)

COVID-19 in pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension: a reference centre survey

Cardiopulmonary exercise testing suggests a beneficial response to pulmonary endarterectomy in a patient with chronic thromboembolic obstruction and normal preoperative pulmonary hemodynamics

Changing demographics, epidemiology, and survival of incident pulmonary arterial hypertension: results from the pulmonary hypertension registry of the United Kingdom and Ireland.

Characterization of GDF2 Mutations and Levels of BMP9 and BMP10 in Pulmonary Arterial Hypertension

Chronic Thromboembolic Pulmonary Hypertension. The Journey from a Curiosity to a Cure

Chronic thromboembolic pulmonary hypertension (CTEPH): results from an international prospective registry

Chronic thromboembolic pulmonary hypertension: advances from bench to patient management

Chronic thromboembolic pulmonary hypertension: role of medical therapy

Chronic thromboembolic pulmonary hypertension: time for research in pathophysiology to catch up with developments in treatment

Connective Tissue Disease–associated Pulmonary Arterial Hypertension in the Modern Treatment Era

Current understanding of the role of bosentan in inoperable chronic thromboembolic pulmonary hypertension

Decreased time constant of the pulmonary circulation in chronic thromboembolic pulmonary hypertension

Demographic features, BMPR2 status and outcomes in distal chronic thromboembolic pulmonary hypertension

Demographics, clinical characteristics, health resource utilization and cost of chronic thromboembolic pulmonary hypertension patients: retrospective results from six European countries.

Determinants of diagnostic delay in Chronic Thromboembolic Pulmonary Hypertension: results from the European CTEPH registry

Developments in pulmonary arterial hypertension-targeted therapy for chronic thromboembolic pulmonary hypertension

Diagnosis, assessment, and treatment of non-pulmonary arterial hypertension pulmonary hypertension

Dual-energy CT angiography for assessment of regional pulmonary perfusion in patients with chronic thromboembolic pulmonary hypertension: initial experience

Dynamic Risk Stratification of Patient Long-Term Outcome After Pulmonary Endarterectomy: Results From the United Kingdom National Cohort

ERS Statement on Chronic Thromboembolic Pulmonary Hypertension

ERS statement on exercise training and rehabilitation in patients with severe chronic pulmonary hypertension

EXPRESS: Acute and chronic dissection of pulmonary artery: new challenges in pulmonary arterial hypertension?

Elevated Levels of Inflammatory Cytokines Predict Survival in Idiopathic and Familial Pulmonary Arterial Hypertension

EmPHasis-10 health-related quality of life score predicts outcomes in patients with idiopathic and connective tissue disease-associated pulmonary arterial hypertension: results from a UK multi-centre study

Endothelin ETA receptors predominate in chronic thromboembolic pulmonary hypertension

Evidence of dysfunction of endothelial progenitors in pulmonary arterial hypertension

Exercise physiological responses to drug treatments in chronic thromboembolic pulmonary hypertension

Functional and haemodynamic outcome 1 year after pulmonary thromboendarterectomy

Genetic determinants of risk and survival in pulmonary arterial hypertension

Genetic determinants of risk in pulmonary arterial hypertension: international genome-wide association studies and meta-analysis

Guidelines on diagnosis and treatment of pulmonary arterial hypertension. The Task Force on Diagnosis and Treatment of Pulmonary Arterial Hypertension of the European Society of Cardiology

Identification of novel rare sequence variation underlying heritable pulmonary arterial hypertension

Identification of rare sequence variation underlying heritable pulmonary arterial hypertension.

Idiopathic pulmonary arterial hypertension and co-existing lung disease: is this a new phenotype?

Impaired Natural Killer Cell Phenotype and Function in Idiopathic and Heritable Pulmonary Arterial Hypertension

Improved Outcomes in Medically and Surgically Treated Chronic Thromboembolic Pulmonary Hypertension

Inefficient exercise gas exchange identifies pulmonary hypertension in chronic thromboembolic obstruction following pulmonary embolism

Interventional and surgical modalities of treatment for pulmonary arterial hypertension

Interventional and surgical modalities of treatment in pulmonary hypertension

Intravenous epoprostenol versus high dose inhaled iloprost for long-term treatment of pulmonary hypertension

Isolated large vessel pulmonary vasculitis as a cause of chronic obstruction of the pulmonary arteries

Lifting the fog in intermediate-risk (submassive) PE: full dose, low dose, or no thrombolysis?

Limitations of resting haemodynamics in chronic thromboembolic disease without pulmonary hypertension

Log-transformation improves the prognostic value of serial NT-proBNP levels in apparently stable pulmonary arterial hypertension

Long-Term Outcome of Patients With Chronic Thromboembolic Pulmonary Hypertension: Results From an International Prospective Registry.

Long-term use of sildenafil in inoperable chronic thromboembolic pulmonary hypertension

Loss-of-Function ABCC8 Mutations in Pulmonary Arterial Hypertension

Maximal cardiac output determines 6 minutes walking distance in pulmonary hypertension

Medical Therapy in Chronic Thromboembolic Pulmonary Hypertension

Medical management of chronic thromboembolic pulmonary hypertension.

Medical therapies for chronic thromboembolic pulmonary hypertension: an evolving treatment paradigm

Medication and patient factors associated with adherence to pulmonary hypertension targeted therapies

Neutrophil Extracellular Traps Promote Angiogenesis: Evidence From Vascular Pathology in Pulmonary Hypertension.

Nitric oxide pathway and phosphodiesterase inhibitors in pulmonary arterial hypertension.

Occlusion pressure analysis role in partitioning of pulmonary vascular resistance in CTEPH

Outcome after cardiopulmonary resuscitation in patients with pulmonary arterial hypertension.

Outcome of pulmonary endarterectomy in symptomatic chronic thromboembolic disease

Patient-reported outcomes assessed by the CAMPHOR questionnaire predict clinical deterioration in idiopathic pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension

Phenotypic Characterization of EIF2AK4 Mutation Carriers in a Large Cohort of Patients Diagnosed Clinically With Pulmonary Arterial Hypertension

Plasma Metabolomics Implicates Modified Transfer RNAs and Altered Bioenergetics in the Outcomes of Pulmonary Arterial Hypertension.

Plasma metabolomics exhibit response to therapy in chronic thromboembolic pulmonary hypertension

Pre-Capillary, Combined, and Post-Capillary Pulmonary Hypertension: A Pathophysiological Continuum

Predicting survival in pulmonary arterial hypertension in the UK.

Presentation and management of pulmonary artery sarcoma

Pulmonary arterial hypertension

Pulmonary arterial hypertension: epidemiology and registries