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List of works by Elena Restelli

A cationic tetrapyrrole inhibits toxic activities of the cellular prion protein.

scientific article published on 15 March 2016

Cell type-specific neuroprotective activity of untranslocated prion protein

scientific article

Cellular prion protein neither binds to alpha-synuclein oligomers nor mediates their detrimental effects

scientific article published on 01 February 2019

Expression of mutant or cytosolic PrP in transgenic mice and cells is not associated with endoplasmic reticulum stress or proteasome dysfunction

scientific article

Mutant PrP suppresses glutamatergic neurotransmission in cerebellar granule neurons by impairing membrane delivery of VGCC α(2)δ-1 Subunit

scientific journal article

Mutant prion protein expression causes motor and memory deficits and abnormal sleep patterns in a transgenic mouse model.

scientific article published in November 2008

Neuroprotective modulation of the unfolded protein response in Marinesco-Sjögren syndrome: PERK signaling inhibition and beyond

scientific article published on 01 January 2019

PERK inhibition attenuates the abnormalities of the secretory pathway and the increased apoptotic rate induced by SIL1 knockdown in HeLa cells

scientific article published on 07 July 2018

PERK inhibition delays neurodegeneration and improves motor function in a mouse model of Marinesco-Sjögren syndrome

scientific article published on 01 July 2018

Synaptic dysfunction in prion diseases: a trafficking problem?

scientific article

Targeting Extracellular Cyclophilin A Reduces Neuroinflammation and Extends Survival in a Mouse Model of Amyotrophic Lateral Sclerosis.

scientific article published on 23 December 2016

Transgenic fatal familial insomnia mice indicate prion infectivity-independent mechanisms of pathogenesis and phenotypic expression of disease

scientific article

Transgenic mice recapitulate the phenotypic heterogeneity of genetic prion diseases without developing prion infectivity: Role of intracellular PrP retention in neurotoxicity

scientific article