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List of works by Paola Rusmini

17-AAG increases autophagic removal of mutant androgen receptor in spinal and bulbar muscular atrophy.

scientific article published on 9 September 2010

A presynaptically toxic secreted phospholipase A2 is internalized into motoneuron-like cells where it is rapidly translocated into the cytosol

scientific article published on 26 January 2008

A role of small heat shock protein B8 (HspB8) in the autophagic removal of misfolded proteins responsible for neurodegenerative diseases

scientific article published on 16 October 2010

ALS-related misfolded protein management in motor neurons and muscle cells

scientific article

Aberrant Autophagic Response in The Muscle of A Knock-in Mouse Model of Spinal and Bulbar Muscular Atrophy.

scientific article

Aggregation and proteasome: the case of elongated polyglutamine aggregation in spinal and bulbar muscular atrophy.

scientific article published on 15 June 2006

Alteration of protein folding and degradation in motor neuron diseases: Implications and protective functions of small heat shock proteins.

scientific article published on 29 September 2011

Androgen-induced neurite outgrowth is mediated by neuritin in motor neurones.

scientific article

Clearance of the mutant androgen receptor in motoneuronal models of spinal and bulbar muscular atrophy.

scientific article published on 28 June 2013

Different anti-aggregation and pro-degradative functions of the members of the mammalian sHSP family in neurological disorders.

scientific article published on 25 March 2013

Differential autophagy power in the spinal cord and muscle of transgenic ALS mice.

scientific article

Dysregulation of axonal transport and motorneuron diseases.

scientific article published on February 2011

Enhanced Clearance of Neurotoxic Misfolded Proteins by the Natural Compound Berberine and Its Derivatives ⬇️

scientific article published on 13 May 2020

Estrogen receptor beta and the progression of prostate cancer: role of 5alpha-androstane-3beta,17beta-diol.

scientific article published on 28 July 2010

Functional interaction between FUS and SMN underlies SMA-like splicing changes in wild-type hFUS mice.

scientific article

Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition)

scientific article

Human adipose-derived mesenchymal stem cells as a new model of spinal and bulbar muscular atrophy.

scientific article

Inhibition of retrograde transport modulates misfolded protein accumulation and clearance in motoneuron diseases.

scientific article published on 12 April 2017

Loss-of-function mutations in the SIGMAR1 gene cause distal hereditary motor neuropathy by impairing ER-mitochondria tethering and Ca2+ signalling

scientific article published on 8 July 2016

Motoneuronal and muscle-selective removal of ALS-related misfolded proteins.

scientific article published on December 2013

Multiple Roles of Transforming Growth Factor Beta in Amyotrophic Lateral Sclerosis

scientific article published on 16 June 2020

Muscle cells and motoneurons differentially remove mutant SOD1 causing familial amyotrophic lateral sclerosis

scientific article

Mutation of SOD1 in ALS: a gain of a loss of function

scientific article

Proteasomal and autophagic degradative activities in spinal and bulbar muscular atrophy.

scientific article published on 16 July 2010

Quantitative assessment of the degradation of aggregated TDP-43 mediated by the ubiquitin proteasome system and macroautophagy

scientific article

Synergic prodegradative activity of Bicalutamide and trehalose on the mutant androgen receptor responsible for spinal and bulbar muscular atrophy

scientific article

Tetracycline-regulated gene expression in the NSC-34-tTA cell line for investigation of motor neuron diseases.

scientific article published on 24 August 2005

The Role of the Heat Shock Protein B8 (HSPB8) in Motoneuron Diseases.

scientific article

The Role of the Protein Quality Control System in SBMA.

scientific article

The anabolic/androgenic steroid nandrolone exacerbates gene expression modifications induced by mutant SOD1 in muscles of mice models of amyotrophic lateral sclerosis

scientific article published on 10 December 2011

The role of the polyglutamine tract in androgen receptor.

scientific article published on 11 September 2007

The small heat shock protein B8 (HSPB8) efficiently removes aggregating species of dipeptides produced in C9ORF72-related neurodegenerative diseases.

scientific article published on 12 June 2017

The small heat shock protein B8 (HSPB8) modulates proliferation and migration of breast cancer cells

scientific article published on 02 January 2017

The small heat shock protein B8 (HspB8) promotes autophagic removal of misfolded proteins involved in amyotrophic lateral sclerosis (ALS).

scientific article published on 22 June 2010

Transcriptional induction of the heat shock protein B8 mediates the clearance of misfolded proteins responsible for motor neuron diseases

scientific article published on 10 March 2016

Trehalose induces autophagy via lysosomal-mediated TFEB activation in models of motoneuron degeneration

scientific article published on 05 November 2018

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