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List of works by Fatima Djouadi

A gender-related defect in lipid metabolism and glucose homeostasis in peroxisome proliferator- activated receptor alpha- deficient mice.

scientific article published on September 1998

A new AMPK activator, GSK773, corrects fatty acid oxidation and differentiation defect in CPT2-deficient myotubes

scientific article published on 01 October 2018

A potential link between peroxisome proliferator-activated receptor signalling and the pathogenesis of arrhythmogenic right ventricular cardiomyopathy.

scientific article

A proof of concept for targeting the PrPC - Amyloid β peptide interaction in basal prostate cancer and mesenchymal colon cancer

scientific article published in 2022

Activation of peroxisome proliferator-activated receptor pathway stimulates the mitochondrial respiratory chain and can correct deficiencies in patients' cells lacking its components

scientific article published on 22 January 2008

Beneficial effects of resveratrol on respiratory chain defects in patients' fibroblasts involve estrogen receptor and estrogen-related receptor alpha signaling

scientific article published on 23 December 2013

Bezafibrate for an inborn mitochondrial beta-oxidation defect.

scientific article published in February 2009

Bezafibrate increases very-long-chain acyl-CoA dehydrogenase protein and mRNA expression in deficient fibroblasts and is a potential therapy for fatty acid oxidation disorders.

scientific article published on 22 August 2005

Birth-related changes in energy metabolism enzymes and Na-K-ATPase in kidney proximal convoluted tubule cells

scientific article published on 01 March 1997

Carnitine palmitoyltransferases 1 and 2: biochemical, molecular and medical aspects

scientific article

Cellular prion protein dysfunction in a prototypical inherited metabolic myopathy

scientific article published on 01 September 2020

Characterization of fatty acid oxidation in human muscle mitochondria and myoblasts.

scientific article

Combination of lipid metabolism alterations and their sensitivity to inflammatory cytokines in human lipin-1-deficient myoblasts

scientific article

Compared effects of missense mutations in Very-Long-Chain Acyl-CoA Dehydrogenase deficiency: Combined analysis by structural, functional and pharmacological approaches.

scientific article

Coordinate development of oxidative enzymes and Na-K-ATPase in thick ascending limb: role of corticosteroids

scientific article published on August 1, 1992

Correction of fatty acid oxidation in carnitine palmitoyl transferase 2-deficient cultured skin fibroblasts by bezafibrate

scientific article published on 2 July 2003

Dietary lipids regulate beta-oxidation enzyme gene expression in the developing rat kidney.

scientific article published on November 1998

Effect of glucocorticoids on mitochondrial oxidative enzyme and Na-K-ATPase activities in the rat proximal tubule and thick ascending limb of Henle

scientific article published on 01 September 1993

Effects of birth on energy metabolism in the rat kidney ⬇️

scientific article published on June 1, 1988

Effects of fatty acids on mitochondrial beta-oxidation enzyme gene expression in renal cell lines

scientific article published on August 2002

Exploring new ways of regulation by resveratrol involving miRNAs, with emphasis on inflammation.

scientific article published on 17 July 2015

Exposure to resveratrol triggers pharmacological correction of fatty acid utilization in human fatty acid oxidation-deficient fibroblasts

scientific article published on 05 March 2011

Fatty acids activate transcription of the muscle carnitine palmitoyltransferase I gene in cardiac myocytes via the peroxisome proliferator-activated receptor alpha

scientific article published on 01 September 1998

Fluxes of nicotinamide adenine dinucleotides through mitochondrial membranes in human cultured cells.

scientific article published on June 1996

GSH monoethyl ester rescues mitochondrial defects in cystic fibrosis models.

scientific article published on 25 April 2011

Genetic basis for correction of very-long-chain acyl-coenzyme A dehydrogenase deficiency by bezafibrate in patient fibroblasts: toward a genotype-based therapy

scientific article published on 29 October 2007

Inhibition of mitophagy drives macrophage activation and anti-bacterial defense during sepsis

scientific article published on 06 August 2020

La β-oxydation mitochondriale des acides gras : une voie métabolique essentielle du fonctionnement musculaire

scientific article published on 01 May 2002

Lack of control by adrenal steroids of oxidative enzymes and Na/K-ATPase development in the rat proximal tubule

scientific article published on 01 July 1993

Long-term follow-up of bezafibrate treatment in patients with the myopathic form of carnitine palmitoyltransferase 2 deficiency.

scientific article published on 26 May 2010

Low-Intensity Running and High-Intensity Swimming Exercises Differentially Improve Energy Metabolism in Mice With Mild Spinal Muscular Atrophy

scientific article published on 01 October 2019

Mitochondrial Fatty Acid β-Oxidation and Resveratrol Effect in Fibroblasts from Patients with Autism Spectrum Disorder

scientific article published in 2021

Mitochondrial Genetic Disorders: Cell Signaling and Pharmacological Therapies.

scientific article published on 28 March 2019

Mitochondrial and metabolic effects of nucleoside reverse transcriptase inhibitors (NRTIs) in mice receiving one of five single- and three dual-NRTI treatments

scientific article published on November 2003

Mitochondrial biogenesis and development of respiratory chain enzymes in kidney cells: role of glucocorticoids.

scientific article published in July 1994

Mitochondrial trifunctional protein deficiency in human cultured fibroblasts: effects of bezafibrate.

scientific article

Mutations in cytokine receptor-like factor 1 (CRLF1) account for both Crisponi and cold-induced sweating syndromes

scientific article

Next generation sequencing of RNA reveals novel targets of resveratrol with possible implications for Canavan disease

scientific article published on 22 October 2018

Organization of the human liver carnitine palmitoyltransferase 1 gene ( CPT1A) and identification of novel mutations in hypoketotic hypoglycaemia

scientific article

Peroxisome proliferator activated receptor delta (PPARdelta) agonist but not PPARalpha corrects carnitine palmitoyl transferase 2 deficiency in human muscle cells

scientific article published on 21 December 2004

Potential of fibrates in the treatment of fatty acid oxidation disorders: Revival of classical drugs?

scientific article published on 01 April 2006

Regulation of fatty acid transport protein and mitochondrial and peroxisomal beta-oxidation gene expression by fatty acids in developing rats

scientific article published on 01 November 2000

Resveratrol and Myopathy

scientific article

Resveratrol attenuates oxidative stress in mitochondrial Complex I deficiency: Involvement of SIRT3.

scientific article

Resveratrol-Induced Changes in MicroRNA Expression in Primary Human Fibroblasts Harboring Carnitine-Palmitoyl Transferase-2 Gene Mutation, Leading to Fatty Acid Oxidation Deficiency.

scientific article published on 22 December 2017

S6 kinase deletion suppresses muscle growth adaptations to nutrient availability by activating AMP kinase

scientific article published in June 2007

Should the beneficial impact of bezafibrate on fatty acid oxidation disorders be questioned?

Species differences in the effects of bezafibrate as a potential treatment of mitochondrial disorders.

scientific article

Specific Physical Exercise Improves Energetic Metabolism in the Skeletal Muscle of Amyotrophic-Lateral- Sclerosis Mice

scientific article published on 20 October 2017

Stilbenes and resveratrol metabolites improve mitochondrial fatty acid oxidation defects in human fibroblasts

scientific article published on 5 June 2014

Succinate dehydrogenase deficiency in human

scientific article

The cellular prion protein controls the mesenchymal-like molecular subtype and predicts disease outcome in colorectal cancer

scientific article published on 31 July 2019

The cellular prion protein is a stress protein secreted by renal tubular cells and a urinary marker of kidney injury

scientific article published on 17 April 2020

The role of PPAR alpha as a "lipostat" transcription factor

scientific article published on 01 January 1999

The role of the peroxisome proliferator-activated receptor alpha (PPAR alpha) in the control of cardiac lipid metabolism

scientific article published on 01 May 1999

Thromboxane synthase mutations in an increased bone density disorder (Ghosal syndrome).

scientific article

Transcriptional regulation by glucocorticoids of mitochondrial oxidative enzyme genes in the developing rat kidney

scientific journal article

[Dysfunctions of mitochondrial fatty acid β-oxidation in rare and common diseases]

scientific article published on 18 October 2019

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