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List of works by Cristin Davidson

A murine Niemann-Pick C1 I1061T knock-in model recapitulates the pathological features of the most prevalent human disease allele

scientific article published on May 2015

Chronic cyclodextrin treatment of murine Niemann-Pick C disease ameliorates neuronal cholesterol and glycosphingolipid storage and disease progression

scientific article

Cyclodextrin alleviates neuronal storage of cholesterol in Niemann-Pick C disease without evidence of detectable blood-brain barrier permeability

scientific article published on 15 February 2013

Endosomal/lysosomal processing of gangliosides affects neuronal cholesterol sequestration in Niemann-Pick disease type C.

scientific article

Identification of Niemann-Pick C1 disease biomarkers through sphingolipid profiling

scientific article published on 23 July 2013

Intracisternal cyclodextrin prevents cerebellar dysfunction and Purkinje cell death in feline Niemann-Pick type C1 disease

scientific article

Intrathecal 2-hydroxypropyl-β-cyclodextrin decreases neurological disease progression in Niemann-Pick disease, type C1: a non-randomised, open-label, phase 1-2 trial

scientific article published on 10 August 2017

Lysosomal compromise and brain dysfunction: examining the role of neuroaxonal dystrophy.

scientific article published on December 2010

Microarray expression analysis and identification of serum biomarkers for Niemann-Pick disease, type C1.

scientific article

Niemann-pick C1 is essential for ebolavirus replication and pathogenesis in vivo.

scientific article published on 26 May 2015

Phenotype assessment for neurodegenerative murine models with ataxia and application to Niemann-Pick disease, type C1

scientific article published on 01 April 2022

Systemic AAV9 gene therapy improves the lifespan of mice with Niemann-Pick disease, type C1.

scientific article

X-linked Angelman-like syndrome caused by Slc9a6 knockout in mice exhibits evidence of endosomal-lysosomal dysfunction.

scientific article published on 29 September 2011

δ-Tocopherol reduces lipid accumulation in Niemann-Pick type C1 and Wolman cholesterol storage disorders

scientific article

δ-Tocopherol reduces lipid accumulation in Niemann-Pick type C1 and Wolman cholesterol storage disorders

scientific article published in Journal of Biological Chemistry

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