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List of works by Vincent Cottin

12q13.12q13.13 microdeletion encompassing ACVRL1 and SCN8A genes: Clinical report of a new contiguous gene syndrome

article

4D time‐resolved magnetic resonance angiography for noninvasive assessment of pulmonary arteriovenous malformations patency

scientific article published on 01 November 2010

A 12-week combination of clarithromycin and prednisone compared to a 24-week prednisone alone treatment in cryptogenic and radiation-induced organizing pneumonia

scientific article published on 28 April 2018

A 2-Year Observational Study in Patients Suffering from Idiopathic Pulmonary Fibrosis and Treated with Pirfenidone: A French Ancillary Study of PASSPORT

scientific article published on 09 April 2019

A Global Survey on Whole Lung Lavage in Pulmonary Alveolar Proteinosis

scientific article published in July 2016

A Standardized Diagnostic Ontology for Fibrotic Interstitial Lung Disease: An International Working Group Perspective.

scientific article published on 17 April 2017

A new era in idiopathic pulmonary fibrosis: considerations for future clinical trials

scientific article published on 21 April 2015

A prospective study of the 6 min walk test as a surrogate marker for haemodynamics in two independent cohorts of treatment-naïve systemic sclerosis-associated pulmonary arterial hypertension

scientific article published on 31 August 2015

ANCA-associated lung fibrosis: analysis of 17 patients

scientific article published on 18 July 2008

Acute Exacerbation of Idiopathic Pulmonary Fibrosis. An International Working Group Report.

scientific article published on 14 June 2016

Acute exacerbation of idiopathic pulmonary fibrosis: international survey and call for harmonisation

scientific article published on 03 April 2020

Acute exacerbation of idiopathic pulmonary fibrosis: shifting the paradigm

scientific article published on August 2015

Adherence to guidelines in idiopathic pulmonary fibrosis: a follow-up national survey

scientific article

Air travel and incidence of pneumothorax in lymphangioleiomyomatosis

scientific article published on 13 December 2018

Alveolar Hemorrhage in Vasculitis (Primary and Secondary)

scientific article published on 01 August 2018

Alveolar Hemorrhage in Vasculitis: Primary and Secondary

scientific article published on June 14, 2011

Alveolar hemorrhage in anti-basement membrane antibody disease: a series of 28 cases

scientific article published on 01 May 2007

Ambivalence of CD4 lymphocytopenia in sarcoidosis

scientific article published on March 1, 2003

An Important Step Forward, but Still a Way to Go

article by Wim A. Wuyts et al published February 2016 in American Journal of Respiratory and Critical Care Medicine

An official American Thoracic Society/European Respiratory Society statement: Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias

scientific article

An official European Respiratory Society/American Thoracic Society research statement: interstitial pneumonia with autoimmune features

scientific article published on 9 July 2015

Analysis of body mass index, weight loss and progression of idiopathic pulmonary fibrosis

scientific article published on 25 November 2020

Angiotensin Receptor Blockers and Subclinical Interstitial Lung Disease: The MESA Study

scientific article published on 01 November 2019

Anti-IgE Monoclonal Antibody (Omalizumab) in Refractory and Relapsing Eosinophilic Granulomatosis With Polyangiitis (Churg-Strauss): Data on Seventeen Patients.

scientific article

Assessment of T-cell polarization on the basis of surface marker expression: Diagnosis and potential therapeutic implications in lymphocytic variant hypereosinophilic syndrome

scientific article published on 13 September 2019

Association between Rheumatoid Arthritis and Pulmonary Hypertension: Data from the French Pulmonary Hypertension Registry

article

Association of Angiotensin Modulators With the Course of Idiopathic Pulmonary Fibrosis

scientific article published on 29 April 2019

Biomarkers of extracellular matrix turnover in patients with idiopathic pulmonary fibrosis given nintedanib (INMARK study): a randomised, placebo-controlled study

scientific article published on 17 July 2019

CC-chemokine ligand 2 inhibition in idiopathic pulmonary fibrosis: a phase 2 trial of carlumab

scientific article published on 22 October 2015

Cancer incidence in patients with pre-capillary pulmonary hypertension

scientific article published on 15 March 2019

Central nervous system involvement in eosinophilic granulomatosis with polyangiitis (Churg-Strauss): Report of 26 patients and review of the literature

scientific article published on 11 July 2017

Centrilobular emphysema combined with pulmonary fibrosis results in improved survival: a response

scientific article published on July 25, 2011

Characterisation of patients with interstitial pneumonia with autoimmune features

scientific article

Characteristics and long-term outcomes of pulmonary veno-occlusive disease induced by Mitomycin-C

scientific article published on 23 September 2020

Chemotherapy is the cornerstone of the combined surgical treatment of lung cancer with synchronous brain metastases

scientific article

Churg-Strauss syndrome presenting with acute myocarditis and cardiogenic shock

scientific article published on 01 October 2011

Clinical characteristics and survival in systemic sclerosis-related pulmonary hypertension associated with interstitial lung disease

scientific article

Clinical highlights from the 2011 ERS Congress in Amsterdam

scientific article published on 9 March 2012

Clinical phenotypes and outcomes of precapillary pulmonary hypertension of sickle cell disease

scientific article published on 04 December 2019

Clinical phenotypes and survival of pre-capillary pulmonary hypertension in systemic sclerosis.

scientific article

Clubbing, Arthralgia and a Large Intrathoracic Mass

scientific article published on June 13, 2012

Coexisting relapsing polychondritis and sarcoidosis: an unusual association

scientific article published on 28 August 2009

Combination therapy: the future of management for idiopathic pulmonary fibrosis?

scientific article

Combined Pulmonary Fibrosis and Emphysema Syndrome in a Patient Age 28 Years with Severe Systemic Sclerosis: Figure 1

scientific article published on 01 September 2011

Combined pulmonary fibrosis and emphysema

scientific article published on 18 April 2007

Combined pulmonary fibrosis and emphysema in connective tissue disease

scientific article published on September 1, 2012

Combined pulmonary fibrosis and emphysema in systemic sclerosis: A syndrome associated with heavy morbidity and mortality

Combined pulmonary fibrosis and emphysema syndrome associated with familial SFTPC mutation

scientific article published on January 19, 2011

Combined pulmonary fibrosis and emphysema syndrome in connective tissue disease

scientific article published in January 2011

Combined pulmonary fibrosis and emphysema: an experimental and clinically relevant phenotype.

scientific article

Combined pulmonary fibrosis and emphysema: bad and ugly all the same?

scientific article

Concomitant medications and clinical outcomes in idiopathic pulmonary fibrosis

scientific article published on 12 December 2019

Conditions associated with severe carbon monoxide diffusion coefficient reduction

scientific article published on March 30, 2011

Connective tissue disease related interstitial lung diseases and idiopathic pulmonary fibrosis: provisional core sets of domains and instruments for use in clinical trials

scientific article

Connective tissue diseases, multimorbidity and the ageing lung

scientific article published on 25 February 2016

Contributors

Corrigendum to: "Portopulmonary hypertension in the current era of pulmonary hypertension management" [J Hepatol (2020);73:130-139]

scientific article published on 07 September 2020

Cough in idiopathic pulmonary fibrosis

scientific article

Cryptogenic organizing pneumonia

scientific article published on 21 September 2012

Current epoprostenol use in patients with severe idiopathic, heritable or anorexigen-associated pulmonary arterial hypertension: data from the French pulmonary hypertension registry

scientific article

Design of a randomised, placebo-controlled clinical trial of nintedanib in patients with systemic sclerosis-associated interstitial lung disease (SENSCIS™).

scientific article

Design of the INPULSIS™ trials: two phase 3 trials of nintedanib in patients with idiopathic pulmonary fibrosis

scientific article published on 29 April 2014

Design of the PF-ILD trial: a double-blind, randomised, placebo-controlled phase III trial of nintedanib in patients with progressive fibrosing interstitial lung disease

scientific article published on 17 September 2017

Desquamative interstitial pneumonia: still orphan and not always benign

scientific article published on 23 June 2020

Diagnosis and management of idiopathic pulmonary fibrosis: French practical guidelines

scientific article published on June 2014

Diagnosis of Idiopathic Pulmonary Fibrosis. An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline

scientific article published on 01 September 2018

Diagnostic Features in Combined Pulmonary Fibrosis and Emphysema (CPFE): A Systematic Review

scientific article published on 01 July 2020

Diagnostic Likelihood Thresholds That Define a Working Diagnosis of Idiopathic Pulmonary Fibrosis

scientific article published on 01 November 2019

Diagnostic accuracy of a clinical diagnosis of idiopathic pulmonary fibrosis: an international case-cohort study.

scientific article

Different phenotypes in dermatomyositis associated with anti-MDA5 antibody: Study of 121 cases

scientific article published on 02 June 2020

Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH) Syndrome and Carcinoid Tumors With/Without NECH: A Clinicopathologic, Radiologic, and Immunomolecular Comparison Study.

scientific article published on 12 February 2018

Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia syndrome

scientific article published on 13 April 2016

Digital Lung Auscultation: Will Early Diagnosis of Fibrotic Interstitial Lung Disease Become a Reality?

scientific article published on 01 July 2019

Diurnal variation in forced vital capacity in patients with fibrotic interstitial lung disease using home spirometry

scientific article published on 01 January 2020

Early Variations of Circulating Interleukin-6 and Interleukin-10 Levels During Thoracic Radiotherapy Are Predictive for Radiation Pneumonitis

Effect of Emphysema Extent on Serial Lung Function in Patients with Idiopathic Pulmonary Fibrosis

scientific article

Effect of cladribine therapy on lung cysts in pulmonary Langerhans cell histiocytosis

scientific article

Effect of pirfenidone on cough in patients with idiopathic pulmonary fibrosis.

scientific article

Effectiveness of cladribine therapy in patients with pulmonary Langerhans cell histiocytosis

scientific article

Efficacy and safety of nintedanib in idiopathic pulmonary fibrosis

scientific article (publication date: 29 May 2014)

Efficacy and safety of rituximab in patients with chronic hypersensitivity pneumonitis (cHP): A retrospective, multicentric, observational study

scientific article published on 09 September 2020

Efficacy of simtuzumab versus placebo in patients with idiopathic pulmonary fibrosis: a randomised, double-blind, controlled, phase 2 trial.

scientific article published on 6 December 2016

Embolization of Recurrent Pulmonary Arteriovenous Malformations by Ethylene Vinyl Alcohol Copolymer (Onyx®) in Hereditary Hemorrhagic Telangiectasia: Safety and Efficacy

scientific article published on 01 July 2022

Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management.

scientific article published on 09 May 2015

Erratum to: Pirfenidone in Idiopathic Pulmonary Fibrosis: Expert Panel Discussion on the Management of Drug-Related Adverse Events.

scientific article published on 8 May 2014

Everolimus for the treatment of lymphangioleiomyomatosis: a phase II study

scientific article published on 25 June 2015

Exogenous lipid pneumonia

scientific article published on 20 November 2006

Exome sequencing and pathogenicity-network analysis of five French families implicate mTOR signalling and autophagy in familial sarcoidosis

scientific article published on 01 August 2019

Familial vs. sporadic sarcoidosis: BTNL2 polymorphisms, clinical presentations, and outcomes in a French cohort

scientific article published on 03 December 2016

Fibrosing interstitial lung diseases: knowns and unknowns

scientific article published on 27 February 2019

Functional assessment and phenotypic heterogeneity of SFTPA1 and SFTPA2 mutations in interstitial lung diseases and lung cancer

scientific article published on 27 August 2020

Future perspectives on rare pulmonary diseases and rare presentations of common disorders

scientific article published in September 2013

Gaps in care of patients living with pulmonary fibrosis: a joint patient and expert statement on the results of a Europe-wide survey

scientific article published on 21 October 2019

Genetics of idiopathic pulmonary fibrosis: from mechanistic pathways to personalised medicine

scientific article published on 23 December 2016

Global effort against rare and orphan diseases

Granulomatosis-associated common variable immunodeficiency disorder: a case-control study versus sarcoidosis

scientific article

Haemodynamics and serial risk assessment in systemic-sclerosis associated pulmonary arterial hypertension

scientific article published on 18 October 2018

Healthcare pathway and patients' expectations in pulmonary fibrosis.

scientific article published on 12 April 2017

Hemodynamic response to treatment and outcome in pulmonary hypertension associated with interstitial lung disease versus pulmonary arterial hypertension in systemic sclerosis

scientific article published on 06 September 2020

Heterozygous RTEL1 mutations are associated with familial pulmonary fibrosis.

scientific article published on 28 May 2015

Home spirometry in patients with idiopathic pulmonary fibrosis: data from the INMARK trial

scientific article published on 08 January 2021

Hot of the breath: Mortality as a primary end-point in IPF treatment trials: the best is the enemy of the good

Hypereosinophilic asthma

scientific article published on 01 March 2011

Hypereosinophilic obliterative bronchiolitis: a distinct, unrecognised syndrome

scientific article published on December 20, 2012

IPF, comorbidities and management implications.

scientific article published on 03 August 2015

Idiopathic inflammatory myopathies and the lung

scientific article published on June 2015

Idiopathic interstitial pneumonia-associated pulmonary hypertension: A target for therapy?

scientific article published on 5 November 2016

Idiopathic non-necrotizing eosinophilic vasculitis limited to the lung: Part of a complex spectrum

scientific article published on 01 July 2020

Idiopathic pulmonary fibrosis

scientific article published on 16 May 2008

Idiopathic pulmonary fibrosis: time for greater expectations?

scientific article published on 02 August 2018

Impact of comorbidities and delay in diagnosis in elderly patients with pulmonary hypertension

Improvement of refractory rheumatoid arthritis-associated constrictive bronchiolitis with etanercept

scientific article published on 01 April 2005

In vivo demonstration of pulmonary microvascular involvement in COVID-19 using Dual-Energy Computed Tomography

scientific article published on 17 September 2020

Initial combination therapy of macitentan and tadalafil in pulmonary arterial hypertension

scientific article published on 29 April 2020

Initial dual oral combination therapy in pulmonary arterial hypertension.

scientific article

Insights into idiopathic pulmonary fibrosis in the real world

scientific article published on 01 July 2015

Interstitial Lung Disease in Idiopathic Inflammatory Myopathy.

scientific article published on May 2010

Interstitial lung disease associated with anti-PM/Scl or anti-aminoacyl-tRNA synthetase autoantibodies: a similar condition?

scientific article published on 15 March 2010

Interstitial lung disease associated with systemic sclerosis (SSc-ILD)

Interstitial lung disease evaluation: detecting connective tissue disease

scientific article published on 08 September 2015

Interstitial lung disease in an adult patient with dermatomyositis and anti-NXP2 autoantibody.

scientific article published in June 2015

Interstitial pneumonia with autoimmune features: Clinical, radiologic, and histological characteristics and outcome in a series of 57 patients

scientific article published on 31 October 2016

Interstitial pneumonia with autoimmune features: the new consensus-based definition for this cohort of patients should be broadened.

scientific article published in April 2016

Interstitial pulmonary amyloidosis

scientific article

Investigating the effects of nintedanib on biomarkers of extracellular matrix turnover in patients with IPF: design of the randomised placebo-controlled INMARK®trial

scientific article published on 20 August 2018

Isolated positive anti-SS-B autoantibodies are not related to clinical features of systemic autoimmune diseases: Results from a routine population survey.

scientific article published on 20 September 2017

Jaagsiekte Sheep Retrovirus (JSRV): from virus to lung cancer in sheep

scientific article

L5. Eosinophilic granulomatosis with polyangiitis (Churg-Strauss).

scientific article published on 09 March 2013

Late-onset sarcoidosis: a comparative study.

scientific article published in May 2012

Long-term clinical and real-world experience with pirfenidone in the treatment of idiopathic pulmonary fibrosis

scientific article published on March 2015

Long-term follow-up in 12 children with pulmonary arteriovenous malformations: confirmation of hereditary hemorrhagic telangiectasia in all cases

scientific article published on 25 July 2007

Long-term safety of pirfenidone: results of the prospective, observational PASSPORT study

scientific article published on 19 October 2018

Lung Diseases in Inflammatory Myopathies

scientific article published on 01 April 2019

Lung Involvement in Rheumatic Disease: Introduction.

scientific article published on 24 June 2015

Lung and heart-lung transplantation for systemic sclerosis patients. A monocentric experience of 13 patients, review of the literature and position paper of a multidisciplinary Working Group

scientific article published on 11 July 2014

Lung biopsy in interstitial lung disease: balancing the risk of surgery and diagnostic uncertainty.

scientific article

Lung cancer in combined pulmonary fibrosis and emphysema: a series of 47 Western patients.

scientific article published on August 2014

Lung function in Birt-Hogg-Dubé syndrome: a retrospective analysis of 96 patients

scientific article published on 24 May 2020

Lung function outcomes in the INPULSIS® trials of nintedanib in idiopathic pulmonary fibrosis

scientific article published on 19 November 2018

Lung-limited or lung-dominant variant of eosinophilic granulomatosis with polyangiitis

scientific article published on 02 March 2020

Lymphangioleiomyomatosis

scientific article published on 26 November 2009

Lymphangioleiomyomatosis Diagnosis and Management: High-Resolution Chest Computed Tomography, Transbronchial Lung Biopsy, and Pleural Disease Management. An Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guideline.

scientific article

MUC5B Promoter Variant and Rheumatoid Arthritis with Interstitial Lung Disease

scientific article published on 20 October 2018

Management and long-term outcomes of sarcoidosis-associated pulmonary hypertension.

scientific article

Many Faces of Bronchiolitis and Organizing Pneumonia

scientific article published on 27 May 2016

Mitomycin-Induced Pulmonary Veno-Occlusive Disease: Evidence From Human Disease and Animal Models

scientific article published on 30 June 2015

Molecular endpoints for establishing target engagement by novel idiopathic pulmonary fibrosis therapies

scientific article published on 18 March 2019

Monoallelic germline ATM mutation and organising pneumonia induced by radiation therapy to the breast

scientific article published on 4 February 2016

Mortality in systemic necrotizing vasculitides: A retrospective analysis of the French Vasculitis Study Group registry

article

Neglected evidence in idiopathic pulmonary fibrosis and the importance of early diagnosis and treatment

scientific article published on March 2014

Neglected evidence in idiopathic pulmonary fibrosis: from history to earlier diagnosis

scientific article published on 18 April 2013

New therapeutic strategies in lung vasculitis: Current Opinion in Pulmonary Medicine, invited review

scientific article published on 27 July 2020

Nintedanib in Progressive Fibrosing Interstitial Lung Diseases

scientific article published on 29 September 2019

Nintedanib in patients with idiopathic pulmonary fibrosis: Combined evidence from the TOMORROW and INPULSIS(®) trials

scientific article

Non-severe eosinophilic granulomatosis with polyangiitis: long-term outcomes after remission-induction trial

scientific article published on 01 December 2019

Nonspecific interstitial pneumonia: time to be more specific?

scientific article

Obstructive sleep apnoea and related comorbidities in incident idiopathic pulmonary fibrosis

scientific article published on 08 June 2017

Occupational hypersensitivity pneumonitis in a baker: a new cause.

scientific article published in April 2014

Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guidelines: Lymphangioleiomyomatosis Diagnosis and Management

scientific article published in September 2016

Orbital mass in ANCA-associated vasculitides: data on clinical, biological, radiological and histological presentation, therapeutic management, and outcome from 59 patients

scientific article published on 01 September 2019

Outcomes following decline in forced vital capacity in patients with idiopathic pulmonary fibrosis: Results from the INPULSIS and INPULSIS-ON trials of nintedanib

scientific article published on 06 August 2019

Parenchymal lung involvement in adult-onset Still disease: A STROBE-compliant case series and literature review

scientific article published on July 2016

Patients' and Healthcare Professionals' Experiences of Idiopathic Pulmonary Fibrosis Treatment with the Pirfenidone 801 mg Tablet Formulation: A Multinational Survey

scientific article published on 19 March 2020

Patients', relatives', and practitioners' views of pulmonary arterial hypertension: A qualitative study

scientific article published on 13 January 2016

Persistent cardiac rhabdomyoma in an adult with tuberous sclerosis.

scientific article published on 14 February 2012

Phenotype and outcome of PAH patients carrying a TBX4 mutation

scientific article published on 20 February 2020

Pilot experience of multidisciplinary team discussion dedicated to inherited pulmonary fibrosis

scientific article published on 03 December 2019

Pirfenidone in idiopathic pulmonary fibrosis: expert panel discussion on the management of drug-related adverse events

scientific article

Pirfenidone in patients with unclassifiable progressive fibrosing interstitial lung disease: a double-blind, randomised, placebo-controlled, phase 2 trial

scientific article published on 29 September 2019

Pirfenidone in patients with unclassifiable progressive fibrosing interstitial lung disease: design of a double-blind, randomised, placebo-controlled phase II trial

scientific article published on 04 September 2018

Pleuroparenchymal fibroelastosis as a late complication of chemotherapy agents

scientific article published on 02 May 2014

Portopulmonary hypertension in the current era of pulmonary hypertension management

scientific article published on 04 March 2020

Practical issues and challenges in idiopathic pulmonary fibrosis

scientific article published on 26 June 2013

Predictors of progression in systemic sclerosis patients with interstitial lung disease

scientific article published on 20 February 2020

Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases

scientific article published on 21 December 2018

Prevalence and characteristics of TERT and TERC mutations in suspected genetic pulmonary fibrosis.

scientific article published on 11 November 2016

Proceedings of the American College of Rheumatology/Association of Physicians of Great Britain and Ireland Connective Tissue Disease-Associated Interstitial Lung Disease Summit: A Multidisciplinary Approach to Address Challenges and Opportunities

scientific article published on 03 January 2019

Proceedings of the American College of Rheumatology/Association of Physicians of Great Britain and Ireland Connective Tissue Disease-Associated Interstitial Lung Disease Summit: A Multidisciplinary Approach to Address Challenges and Opportunities

scientific article published on 01 February 2019

Professional exposure to goats increases the risk of pneumonic-type lung adenocarcinoma: results of the IFCT-0504-Epidemio study

scientific article

Prognostic value of right ventricular ejection fraction in pulmonary arterial hypertension

scientific article published on 23 December 2014

Progression of idiopathic pulmonary fibrosis: lessons from asymmetrical disease

scientific article published on September 29, 2010

Progressive fibrosing interstitial lung disease: a clinical cohort (the PROGRESS® study)

scientific article published on 17 September 2020

Progressive fibrosing interstitial lung disease: clinical uncertainties, consensus recommendations, and research priorities

scientific article published on 01 September 2020

Progressive fibrosing interstitial lung diseases: current practice in diagnosis and management

scientific article published on 02 August 2019

Prolidase deficiency: a new genetic cause of combined pulmonary fibrosis and emphysema syndrome in the adult

scientific article published on 09 April 2020

Pulmonary Arterial Hypertension Associated With Systemic Lupus Erythematosus: Results From the French Pulmonary Hypertension Registry

scientific article published on 26 August 2017

Pulmonary Vein Varices Are Syndromic Features in Turner Syndrome

scientific article published on 3 May 2017

Pulmonary alveolar proteinosis

scientific article published on 7 March 2019

Pulmonary alveolar proteinosis following cryptococcal meningitis: a possible cause?

scientific article

Pulmonary arterial hypertension in heroin users.

scientific article published on 31 March 2016

Pulmonary arterial hypertension in idiopathic inflammatory myopathies: Data from the French pulmonary hypertension registry and review of the literature

scientific article

Pulmonary arteriovenous malformations in hereditary hemorrhagic telangiectasia: a series of 126 patients

scientific article published on 01 January 2007

Pulmonary arteriovenous malformations in patients with hereditary hemorrhagic telangiectasia

scientific article published on 23 January 2004

Pulmonary fibrosis: "idiopathic" is not "cryptogenic"

scientific article published on 18 March 2019

Pulmonary hypertension associated with benfluorex exposure

scientific article published on 20 April 2012

Pulmonary hypertension in chronic lung diseases: comparison to other pulmonary hypertension groups.

scientific article

Pulmonary hypertension in interstitial lung diseases: diagnostic and therapeutic approach in 2011?

scientific article published on 01 April 2011

Pulmonary hypertension in lymphangioleiomyomatosis: characteristics in 20 patients

scientific article published on 23 February 2012

Pulmonary hypertension-specific therapy in patients with chronic respiratory insufficiency

scientific article published on 01 September 2014

Pulmonary rheumatoid nodule

scientific article published on 19 June 2007

Pulmonary varix mimicking pulmonary arteriovenous malformation in a patient with Turner syndrome

scientific article

Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (rendu-osler disease).

scientific article published on January 2007

Quantification of myocardial extracellular volume fraction with cardiac MR imaging for early detection of left ventricle involvement in systemic sclerosis

article by Franck Thuny et al published May 2014 in Radiology

Rare (pulmonary) disease day: "feeding the breath, energy for life!".

scientific article published in February 2015

Rare lung disease and orphan drug development

scientific article published on 25 June 2013

Rare pulmonary diseases and orphan drugs: where do we stand and where are we going to?

scientific article

Recent advances in the pathobiology and clinical management of lymphangioleiomyomatosis

scientific article published on 01 September 2018

Recent lessons learned in the management of acute exacerbation of idiopathic pulmonary fibrosis

scientific article

Regulator of telomere length 1 (RTEL1) mutations are associated with heterogeneous pulmonary and extra-pulmonary phenotypes

scientific article published on 07 February 2019

Renal involvement in eosinophilic granulomatosis with polyangiitis (EGPA): a multicentric retrospective study of 63 biopsy-proven cases

scientific article published on 28 August 2020

Reply: The ATS/JRS Guidelines on Lymphangioleiomyomatosis: Filling in the Gaps.

scientific article published on 13 March 2017

Respiratory manifestations of eosinophilic granulomatosis with polyangiitis (Churg-Strauss).

scientific article

Response to Letter Regarding Article, “Mitomycin-Induced Pulmonary Veno-Occlusive Disease: Evidence From Human Disease and Animal Model”

scientific article published on 01 April 2016

Review of IPF diagnosis and management recommendations in Europe

scientific article published on 17 December 2013

Revisiting the systemic vasculitis in eosinophilic granulomatosis with polyangiitis (Churg-Strauss): A study of 157 patients by the Groupe d'Etudes et de Recherche sur les Maladies Orphelines Pulmonaires and the European Respiratory Society Taskforc

scientific article published on 23 September 2016

Right isovolumic contraction velocity predicts survival in pulmonary hypertension

scientific article published on 21 December 2012

Right-to-left shunt with hypoxemia in pulmonary hypertension

scientific article

Riociguat for idiopathic interstitial pneumonia-associated pulmonary hypertension (RISE-IIP): a randomised, placebo-controlled phase 2b study

scientific article published on 12 August 2019

Risk Factors for Mortality Following COVID-19 in Patients with Pre-existing Interstitial Lung Disease

scientific article published on 30 November 2020

Risk assessment, prognosis and guideline implementation in pulmonary arterial hypertension

scientific article published on 3 August 2017

Risk factors for disease progression in idiopathic pulmonary fibrosis

scientific article published on 14 October 2019

Risk of Direct Oral Anticoagulant Bioaccumulation in Patients with Pulmonary Hypertension

scientific article published on 16 April 2016

Rituximab for auto-immune alveolar proteinosis, a real life cohort study.

scientific article published on 25 April 2018

Role of atmospheric pollution on the natural history of idiopathic pulmonary fibrosis.

scientific article published on 10 August 2017

SARCOIDOSIS DIAGNOSED IN THE ELDERLY: A CASE CONTROL STUDY

scientific article published on 22 June 2020

SFTPC mutations in patients with familial pulmonary fibrosis: combined with emphysema?

scientific article published on 01 April 2011

Safety and efficacy of pirfenidone and nintedanib in patients with Idiopathic Pulmonary Fibrosis and carrying a telomere related gene mutation

scientific article published on 19 November 2020

Safety and efficacy of pirfenidone in patients carrying telomerase complex mutation

scientific article published on 15 February 2018

Safety of right heart catheterization for pulmonary hypertension in very elderly patients

Screening for lung cancer and idiopathic pulmonary fibrosis: killing two birds with one stone

scientific article published in February 2014

Selected clinical highlights from the 2012 ERS congress in Vienna

scientific article published on 6 December 2012

Severe Prolonged Cough as Presenting Manifestation of FIP1L1-PDGFRA+ Chronic Eosinophilic Leukaemia: A Widely Ignored Association

scientific article published on 12 May 2016

Severe hematologic complications after lung transplantation in patients with telomerase complex mutations

scientific article

Severe pulmonary hypertension associated with COPD: hemodynamic improvement with specific therapy

scientific article published on 5 August 2015

Shared genetic predisposition in rheumatoid arthritis-interstitial lung disease and familial pulmonary fibrosis.

scientific article

Should Patients With Interstitial Lung Disease Be Seen by Experts?

scientific article published on 01 September 2018

Should we screen for pulmonary hypertension at the initial evaluation of idiopathic pulmonary fibrosis?

scientific article published on 29 March 2013

Spectrum and prognosis of ANCA-associated vasculitis-related bronchiectasis: data from 61 patients

scientific article published on 01 December 2019

Spectrum of Fibrotic Lung Diseases

scientific article published on 01 September 2020

Spontaneous pneumomediastinum associated with pneumorachis

scientific article published in June 2014

Statin Therapy and Outcomes in Trials of Nintedanib in Idiopathic Pulmonary Fibrosis.

scientific article published on 7 February 2018

Study protocol: exploring the efficacy of cyclophosphamide added to corticosteroids for treating acute exacerbation of idiopathic pulmonary fibrosis; a randomized double-blind, placebo-controlled, multi-center phase III trial (EXAFIP)

Subclinical Interstitial Lung Disease: No Place for Crackles?

scientific article published on August 1, 2012

Subclinical venous access infection and clinical worsening in pulmonary arterial hypertension.

scientific article

Survey of Physician's Knowledge, Attitudes, and Practices Regarding Idiopathic Pulmonary Fibrosis in Turkey

scientific article published on 01 January 2020

Survival Improved in Patients Aged ≤ 70 Years With Systemic Sclerosis-Associated Pulmonary Arterial Hypertension During the Period 2006 to 2017 in France

scientific article published on 19 November 2019

Survival in patients with idiopathic, familial, and anorexigen-associated pulmonary arterial hypertension in the modern management era.

scientific article

Symptomatic muscular sarcoidosis: Lessons from a nationwide multicenter study.

scientific article published on 16 March 2018

Synchronous small-cell lung cancer and gastrointestinal stromal tumor: a case report

scientific article published on 22 November 2008

Syndrome of pleural and retrosternal "bridging" fibrosis and retroperitoneal fibrosis in patients with asbestos exposure

scientific article published on 2 February 2009

Targeting interleukin-13 in idiopathic pulmonary fibrosis: from promising path to dead end

scientific article published on 13 December 2018

The Ariane-IPF ERS Clinical Research Collaboration: seeking collaboration through launch of a federation of European registries on idiopathic pulmonary fibrosis

scientific article published on 23 May 2019

The Challenge of Acute Exacerbation of Pulmonary Fibrosis

scientific article published on September 16, 2011

The Lung in Hereditary Hemorrhagic Telangiectasia.

scientific article published on 30 August 2017

The Lung in Rheumatoid Arthritis: Focus on Interstitial Lung Disease

scientific article published on 04 September 2018

The MUC5B variant is associated with idiopathic pulmonary fibrosis but not with systemic sclerosis interstitial lung disease in the European Caucasian population

scientific article

The Respiratory System in Autoimmune Vascular Diseases

scientific article published on 04 July 2018

The challenge of criteria for interstitial pneumonia with autoimmune features

scientific article published on 06 April 2017

The clinical phenotype associated with myositis-specific and associated autoantibodies: a meta-analysis revisiting the so-called antisynthetase syndrome

scientific article published on 03 April 2014

The natural history of progressive fibrosing interstitial lung diseases

scientific article published on 26 March 2020

The pathogenesis of pulmonary fibrosis: a moving target

scientific article published on 25 October 2012

The syndrome of combined pulmonary fibrosis and emphysema

scientific article published on 01 July 2009

The threat in chronic lung diseases: acute exacerbations

scientific article

The unmet medical need of pulmonary hypertension in idiopathic pulmonary fibrosis

scientific article published on 18 January 2018

The yin and yang of idiopathic pulmonary fibrosis

scientific article published on 23 February 2017

Therapeutic effects of nintedanib are not influenced by emphysema in the INPULSIS trials

scientific article published on 18 April 2019

Thoracic manifestations of segmental neurofibromatosis

scientific article published on 25 September 2017

Tracheobronchial Stenoses in Granulomatosis With Polyangiitis (Wegener's): A Report on 26 Cases

scientific article

Translation and validation of the King's Brief Interstitial Lung Disease (K-BILD) questionnaire in French, Italian, Swedish, and Dutch.

scientific article published in January 2016

Treatment of idiopathic inflammatory myositis associated interstitial lung disease: A systematic review and meta-analysis

scientific article published on 17 December 2018

Treatment of idiopathic pulmonary fibrosis with etanercept: an exploratory, placebo-controlled trial

scientific article published on 31 July 2008

Treatment of progressive fibrosing interstitial lung diseases: a milestone in the management of interstitial lung diseases

scientific article published on 01 September 2019

Understanding the priorities for women diagnosed with lymphangioleiomyomatosis: a patient perspective

scientific article

Unusual bilateral acinar nodules: case for diagnosis

scientific article published on 06 March 2009

Upfront triple combination therapy in pulmonary arterial hypertension: a pilot study

scientific article published on 13 March 2014

Use of Biologics to Treat Relapsing and/or Refractory Eosinophilic Granulomatosis with Polyangiitis: data from a European Collaborative Study

scientific article published on 01 October 2020

Usual interstitial pneumonia end-stage features from explants with radiologic and pathological correlations

scientific article published on 13 May 2015

Usual interstitial pneumonia in ANCA-associated vasculitis: A poor prognostic factor

scientific article published on 27 September 2019

Validation of multidisciplinary diagnosis in IPF.

scientific article published in February 2018

Velcro crackles: the key for early diagnosis of idiopathic pulmonary fibrosis?

scientific article published on September 1, 2012

Vinblastine chemotherapy in adult patients with langerhans cell histiocytosis: a multicenter retrospective study

scientific article

When to stop in the quest of formes frustes of connective tissue disease?

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