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List of works by Scott Bell

'Iron lung': distinctive bronchoscopic features of acute iron tablet aspiration

scientific article published on 01 December 2003

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation

scientific article published on November 2011

A Novel Method and Its Application to Measuring Pathogen Decay in Bioaerosols from Patients with Respiratory Disease

scientific article published in 2016

A Rapid Pipeline to Model Rare Neurodevelopmental Disorders with Simultaneous CRISPR/Cas9 Gene Editing

scientific article published on December 2016

A comparison of two informative SNP-based strategies for typing Pseudomonas aeruginosa isolates from patients with cystic fibrosis

scientific article

A d-optimal designed population pharmacokinetic study of oral itraconazole in adult cystic fibrosis patients

scientific article

A de novo frameshift mutation in chromodomain helicase DNA-binding domain 8 (CHD8): A case report and literature review.

scientific article

A new phase of CFTR treatment for cystic fibrosis?

scientific article published on 22 July 2015

A phase 3, multi-center, multinational, randomized, double-blind, placebo-controlled study to evaluate the efficacy and safety of levofloxacin inhalation solution (APT-1026) in stable cystic fibrosis patients

scientific article

A phase 3, open-label, randomized trial to evaluate the safety and efficacy of levofloxacin inhalation solution (APT-1026) versus tobramycin inhalation solution in stable cystic fibrosis patients

scientific article published on 13 January 2015

Abnormalities of the PTH-vitamin D axis and bone turnover markers in children, adolescents and adults with cystic fibrosis: comparison with healthy controls

scientific article published on 8 April 2003

Abolition of Pseudomonas aeruginosa AUST-01 from an Australian CF center: Do other strains remain?

scientific article published on 11 February 2019

Accurate assessment of systemic iron status in cystic fibrosis will avoid the hazards of inappropriate iron supplementation.

scientific article published on 22 October 2012

Activation and adoptive transfer of Epstein-Barr virus-specific cytotoxic T cells in solid organ transplant patients with posttransplant lymphoproliferative disease.

scientific article published on August 1999

Anomalies in T Cell Function Are Associated With Individuals at Risk of Mycobacterium abscessus Complex Infection.

scientific article

Antibiotic desensitization in adults with cystic fibrosis.

scientific article

Antibiotic perturbation of mixed-strain Pseudomonas aeruginosa infection in patients with cystic fibrosis

scientific article published on 2 November 2017

Antibiotic susceptabilities of Pseudomonas aeruginosa isolates derived from patients with cystic fibrosis under aerobic, anaerobic, and biofilm conditions.

scientific article

Antimicrobial resistance in cystic fibrosis: Does it matter?

scientific article published on 27 September 2018

Antimicrobial treatment of non-cystic fibrosis bronchiectasis

scientific article

Aztreonam for inhalation solution, challenges to drug approval and integration into CF care

scientific article published on September 19, 2012

Beta-lactam allergy in adults with cystic fibrosis.

scientific article published on 19 December 2006

Beyond borders: cystic fibrosis survival between Australia, Canada, France and New Zealand

Biomarkers: Their Role in CFTR Modulator Therapies from Early Development to the Clinic

scientific article

Bone mineral density in Australian children, adolescents and adults with cystic fibrosis: a controlled cross sectional study.

scientific article published on February 2004

Bronchiectasis: Yet another systemic disease?

scientific article published on 02 May 2018

Burkholderia cepacia complex epidemiology in persons with cystic fibrosis from Australia and New Zealand.

scientific article

Burkholderia pseudomallei: another emerging pathogen in cystic fibrosis

scientific article published on December 2003

Burkholderia stagnalis sp. nov. and Burkholderia territorii sp. nov., two novel Burkholderia cepacia complex species from environmental and human sources

scientific article

CFTR-dependent defect in alternatively-activated macrophages in cystic fibrosis.

scientific article published on 17 April 2017

Can tumor necrosis factor-alpha (TNF-alpha) be reliably measured in blood?

scientific article published on 01 April 1995

Chronic suppurative lung disease and bronchiectasis in children and adults in Australia and New Zealand Thoracic Society of Australia and New Zealand guidelines

scientific article published on January 2015

Chronic suppurative lung disease and bronchiectasis in children and adults in Australia and New Zealand Thoracic Society of Australia and New Zealand guidelines.

scientific article

Clinical presentation of metabolic alkalosis in an adult patient with cystic fibrosis.

scientific article

Clinical utilization of genomics data produced by the international Pseudomonas aeruginosa consortium

scientific article

Clonal complex Pseudomonas aeruginosa in horses.

scientific article

Clostridium difficile infection in cystic fibrosis: an uncommon but life-threatening complication

scientific article published on 07 December 2016

Comparison of the US and Australian cystic fibrosis registries: the impact of newborn screening.

scientific article published on 16 January 2012

Control of Confounding and Reporting of Results in Causal Inference Studies: Guidance for Authors from Editors of Respiratory, Sleep, and Critical Care Journals

Controlled longitudinal study of bone mass accrual in children and adolescents with cystic fibrosis.

scientific article

Cough-generated aerosols of Pseudomonas aeruginosa and other Gram-negative bacteria from patients with cystic fibrosis.

scientific article

Current infection control practices used in Australian and New Zealand cystic fibrosis centers

scientific article published on 17 January 2020

Cystic fibrosis

scientific article published on 14 May 2015

Cystic fibrosis in Australia, 2009: results from a data registry

scientific article

Cystic fibrosis pathogens survive for extended periods within cough-generated droplet nuclei.

scientific article

Daily versus weekly azithromycin in cystic fibrosis patients

scientific article published on 30 May 2007

Death after lung transplantation in cystic fibrosis patients infected with Burkholderia cepacia

scientific article published on 01 February 2009

Defining antimicrobial resistance in cystic fibrosis

scientific article published on 25 September 2018

Differential expression of genes and receptors in monocytes from patients with cystic fibrosis

article

Disruption of GRIN2B Impairs Differentiation in Human Neurons

ECFS best practice guidelines: the 2018 revision

scientific article published on 2 March 2018

Early Intervention of Cystic Fibrosis Pulmonary Exacerbations Based on Home Monitoring. eICE through the Looking Glass

scientific article

Effect of Nerve Stimulation Use on the Success Rate of Ultrasound-Guided Subsartorial Saphenous Nerve Block: A Randomized Controlled Trial

scientific article published on 29 November 2016

Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: a randomised trial.

scientific article published on March 2002

Effect of temperature on cystic fibrosis lung disease and infections: a replicated cohort study

scientific article

Elevated metal concentrations in the CF airway correlate with cellular injury and disease severity.

scientific article

Emergence and spread of a human-transmissible multidrug-resistant nontuberculous mycobacterium

scientific article published in November 2016

Energy cost of physical activity in cystic fibrosis

scientific article published on 01 August 2001

Epidemiological analysis of methicillin-resistant Staphylococcus aureus isolates from adult patients with cystic fibrosis.

scientific article published on 8 February 2006

European Cystic Fibrosis Society Standards of Care: Best Practice guidelines

scientific article published on May 2014

Evaluation of phenotypic screening tests for carbapenemase production in Pseudomonas aeruginosa from patients with cystic fibrosis

scientific article published on 10 February 2015

Evidence for opioid modulation and generation of prostaglandins in sulphur dioxide (SO)2-induced bronchoconstriction

scientific article published on February 1996

Evidence for spread of a clonal strain of Pseudomonas aeruginosa among cystic fibrosis clinics

scientific article published on May 2003

Ex vivo monitoring of human cytomegalovirus-specific CD8+ T-cell responses using QuantiFERON-CMV.

scientific article

Exacerbations in cystic fibrosis: 2 . prevention.

scientific article

Exercise testing in patients with cystic fibrosis: Why and which?

article

Expression of Pseudomonas aeruginosa Antibiotic Resistance Genes Varies Greatly during Infections in Cystic Fibrosis Patients

article

Face Masks and Cough Etiquette Reduce the Cough Aerosol Concentration of Pseudomonas aeruginosa in People with Cystic Fibrosis.

scientific article published on 20 September 2017

Factors influencing acquisition of Burkholderia cepacia complex organisms in patients with cystic fibrosis

scientific article

Gaming console exercise and cycle or treadmill exercise provide similar cardiovascular demand in adults with cystic fibrosis: a randomised cross-over trial

scientific article published on 01 January 2011

Gene expression characteristics of a cystic fibrosis epidemic strain of Pseudomonas aeruginosa during biofilm and planktonic growth

scientific article

Gene-environmental interaction in asthma

scientific article published on February 2007

Genetic modifiers of liver disease in cystic fibrosis

scientific article

Genomic and phenotypic comparison of environmental and patient-derived isolates of Pseudomonas aeruginosa suggest that antimicrobial resistance is rare within the environment

scientific article published on 01 November 2019

Genomovar diversity amongst Burkholderia cepacia complex isolates from an Australian adult cystic fibrosis unit

scientific article published on 27 June 2003

Genotypic Diversity within a Single Pseudomonas aeruginosa Strain Commonly Shared by Australian Patients with Cystic Fibrosis

scientific article

Geographical differences in first acquisition of Pseudomonas aeruginosa in cystic fibrosis.

scientific article

High ambient temperature and risk of intestinal obstruction in cystic fibrosis.

scientific article published on April 2016

High prevalence of a class 1 integron-associated aadB gene cassette in Pseudomonas aeruginosa isolates from an Australian cystic fibrosis patient population

scientific article published in August 2008

High-throughput single-nucleotide polymorphism-based typing of shared Pseudomonas aeruginosa strains in cystic fibrosis patients using the Sequenom iPLEX platform

scientific article

Human epididymis protein 4 (HE4) levels inversely correlate with lung function improvement (delta FEV1) in cystic fibrosis patients receiving ivacaftor treatment

scientific article published on 27 September 2018

ICU outcomes in cystic fibrosis following invasive ventilation

scientific article published on 01 May 2013

Identification of Pseudomonas aeruginosa by a duplex real-time polymerase chain reaction assay targeting the ecfX and the gyrB genes

scientific article published on 21 November 2008

Identification of an unusual Brucella strain (BO2) from a lung biopsy in a 52 year-old patient with chronic destructive pneumonia.

scientific article

Idiosyncratic reactions are the most common cause of abnormal liver function tests in patients with cystic fibrosis

scientific article published on April 2015

Implication of LRRC4C and DPP6 in neurodevelopmental disorders

scientific article published on 19 October 2016

Importance of hepatic fibrosis in cystic fibrosis and the predictive value of liver biopsy

scientific article published on 17 November 2010

Infection in cystic fibrosis: impact of the environment and climate.

scientific article published on 7 March 2016

Infection risks for patients from healthcare workers with cystic fibrosis - Reply

scientific article published on 04 February 2019

Inhaled antibiotics in Cystic Fibrosis (CF) and non-CF bronchiectasis.

scientific article published on 31 March 2015

Inhaled corticosteroids for bronchiectasis

scientific article published on 16 May 2018

Inhaled steroids for bronchiectasis

scientific article

Intravenous aminoglycoside usage and monitoring of patients with cystic fibrosis in Australia. What's new?

scientific article published on 16 August 2008

Ivacaftor in severe cystic fibrosis lung disease and a G551D mutation.

scientific article

JCF - 2014 and beyond

scientific article published on 08 November 2014

Learning's from the Editors Desk - 2017.

scientific article published in November 2017

Lesch-Nyhan Syndrome: Models, Theories, and Therapies.

scientific article published on 24 September 2016

Low rates of Pseudomonas aeruginosa misidentification in isolates from cystic fibrosis patients

scientific article

Lower airway microbiota for ‘biomarker’ measurements of cystic fibrosis disease progression?

scientific article published on 22 August 2018

Lumacaftor/Ivacaftor Treatment of Patients with Cystic Fibrosis Heterozygous for F508del-CFTR.

scientific article published on 29 November 2016

MRSA eradication in a health care worker with cystic fibrosis; re-emergence or re-infection?

scientific article published in September 2005

Management of comorbidities in older patients with cystic fibrosis.

scientific article published on 19 March 2013

Metabolic and inflammatory responses to pulmonary exacerbation in adults with cystic fibrosis

article

Methicillin-resistant Staphylococcus aureus acquisition in healthcare workers with cystic fibrosis: a retrospective cross-sectional study.

scientific article

Molecular Imprint of Exposure to Naturally Occurring Genetic Variants of Human Cytomegalovirus on the T cell Repertoire

scientific article published on 10 February 2014

Molecular surveillance for carbapenemase genes in carbapenem-resistant Pseudomonas aeruginosa in Australian patients with cystic fibrosis

scientific article published on February 2015

Multi-centre research in Australia: analysis of a recent National Health and Medical Research Council-funded project.

scientific article published in September 2009

Mutations in the HFE gene can be associated with increased lung disease severity in cystic fibrosis

article

Narrowing of T-cell receptor beta variable repertoire during symptomatic herpesvirus infection in transplant patients.

scientific article published on 6 October 2009

Neutrophils in cystic fibrosis.

scientific article published on January 2009

New insights into gene-specific management in cystic fibrosis from the 2012 European Cystic Fibrosis Conference

scientific article published on 01 November 2012

New pharmacological approaches for cystic fibrosis: promises, progress, pitfalls.

scientific article

Non-invasive ventilation used as an adjunct to airway clearance treatments improves lung function during an acute exacerbation of cystic fibrosis: a randomised trial

scientific article published on 18 June 2015

Non-invasive ventilation versus oxygen therapy in cystic fibrosis: A 12-month randomized trial

scientific article published on 17 June 2019

Novel application of biological glue in the management of a complicated pneumothorax in cystic fibrosis

article

Nutrition in adults with cystic fibrosis

scientific article published on 01 October 1998

On tumor necrosis factor alpha in CF

scientific article published on 01 June 1994

Optimising nutrition in cystic fibrosis

scientific article published on 01 June 2002

Pathogen to commensal? Longitudinal within-host population dynamics, evolution, and adaptation during a chronic >16-year Burkholderia pseudomallei infection

scientific article published on 05 March 2020

Phenotypic characterization of clonal and nonclonal Pseudomonas aeruginosa strains isolated from lungs of adults with cystic fibrosis

scientific article published on 28 March 2007

Population Pharmacokinetics of Itraconazole and its Active Metabolite Hydroxy-Itraconazole in Paediatric Cystic Fibrosis and Bone Marrow Transplant Patients

scientific article published on 01 January 2006

Predictors of pulmonary exacerbations in patients with cystic fibrosis infected with multi-resistant bacteria.

scientific article

Pregnancy and cystic fibrosis: Approach to contemporary management.

scientific article

Protease IV production in Pseudomonas aeruginosa from the lungs of adults with cystic fibrosis

scientific article published in December 2006

Pseudomonas aeruginosa antibiotic resistance in Australian cystic fibrosis centres

scientific article

Pseudomonas aeruginosa exhibits frequent recombination, but only a limited association between genotype and ecological setting.

scientific article

Pseudomonas aeruginosa genotypes acquired by children with cystic fibrosis by age 5-years

scientific article published on 3 January 2015

Pubertal development and its influences on bone mineral density in Australian children and adolescents with cystic fibrosis

scientific article published in July 2005

Pulmonary artery enlargement and cystic fibrosis pulmonary exacerbations: a cohort study

scientific article published on 9 June 2016

Pulmonary eosinophilia associated with aminoglutethimide

scientific article published on 01 October 1998

Pulmonary exacerbations in cystic fibrosis and bronchiectasis

scientific article published on April 2007

Pyrosequencing reveals transient cystic fibrosis lung microbiome changes with intravenous antibiotics.

scientific article

Randomized Trial of a Decision Aid for Patients with Cystic Fibrosis Considering Lung Transplantation

scientific article published on 09 July 2009

Rapid genotyping of Pseudomonas aeruginosa isolates harboured by adult and paediatric patients with cystic fibrosis using repetitive-element-based PCR assays.

scientific article published in November 2004

Rapid single-nucleotide polymorphism-based identification of clonal Pseudomonas aeruginosa isolates from patients with cystic fibrosis by the use of real-time PCR and high-resolution melting curve analysis

scientific article published on 28 January 2011

Reconciling Antimicrobial Susceptibility Testing and Clinical Response in Antimicrobial Treatment of Chronic Cystic Fibrosis Lung Infections

scientific article published in October 2019

Reconstitution of the latent T-lymphocyte response to Epstein-Barr virus is coincident with long-term recovery from posttransplant lymphoma after adoptive immunotherapy

scientific article published in May 2003

Reduced mucosal associated invariant T-cells are associated with increased disease severity and Pseudomonas aeruginosa infection in cystic fibrosis.

scientific article

Repeatability and methodology of resting energy expenditure in patients with cystic fibrosis.

scientific article published in May 1999

Reply to: Use of Masks in Cystic Fibrosis Patients

scientific article published on 20 September 2018

Reply: More on Causal Inference Studies

scientific article published on 01 May 2019

Report of the European Respiratory Society/European Cystic Fibrosis Society task force on the care of adults with cystic fibrosis

scientific article published on 09 October 2015

Resting energy expenditure and oxygen cost of breathing in patients with cystic fibrosis.

scientific article published on February 1996

Rifampicin and sodium fusidate reduces the frequency of methicillin-resistant Staphylococcus aureus (MRSA) isolation in adults with cystic fibrosis and chronic MRSA infection.

scientific article published in March 2004

Room ventilation and the risk of airborne infection transmission in 3 health care settings within a large teaching hospital.

scientific article

Sexual and reproductive health in men with cystic fibrosis: consistent preferences, inconsistent practices.

scientific article published on 12 June 2009

Shared Pseudomonas aeruginosa genotypes are common in Australian cystic fibrosis centres

scientific article published on 9 August 2012

Sources and dynamics of fluorescent particles in hospitals

scientific article published on 17 March 2017

Sputum neutrophils in cystic fibrosis patients display a reduced respiratory burst.

scientific article published on 23 December 2012

Sub-inhibitory concentrations of ceftazidime and tobramycin reduce the quorum sensing signals of Pseudomonas aeruginosa

scientific article

Sugar sweet and deadly?

scientific article published in March 2009

The Cystic Fibrosis Foundation Patient Registry. Design and Methods of a National Observational Disease Registry

scientific article published on 01 July 2016

The changing prevalence of pulmonary infection in adults with cystic fibrosis: A longitudinal analysis

scientific article published on 8 August 2016

The effects of climate and air pollution on people with chronic lung disease in Australia

scientific article published in 2019

The experience of men and women with cystic fibrosis who have become a parent: a qualitative study

scientific article published on 21 December 2017

The month of July: an early experience with pandemic influenza A (H1N1) in adults with cystic fibrosis

scientific article

The role of anaerobic bacteria in the cystic fibrosis airway.

scientific article published on 21 July 2016

The social network of cystic fibrosis centre care and shared Pseudomonas aeruginosa strain infection: a cross-sectional analysis

scientific article published on 21 July 2015

The treatment of the pulmonary and extrapulmonary manifestations of cystic fibrosis

scientific article published on 30 May 2017

Transcriptomic analysis of longitudinal Burkholderia pseudomallei infecting the cystic fibrosis lung

scientific article published on 10 July 2018

Transition of adolescents with cystic fibrosis from paediatric to adult care

scientific article published on 10 November 2010

Transmission of bacteria in bronchiectasis and chronic obstructive pulmonary disease: Low burden of cough aerosols

scientific article published on 27 March 2019

Treatment decisions for MRSA in patients with cystic fibrosis (CF): when is enough, enough?

scientific article published on 11 January 2017

Trepopnoea due to positional narrowing of the left main bronchus

scientific article published on 01 December 1999

Tropical Australia is a potential reservoir of non-tuberculous mycobacteria in cystic fibrosis

scientific article published on 11 May 2017

Viability of Pseudomonas aeruginosa in cough aerosols generated by persons with cystic fibrosis.

scientific article published on 17 April 2014

Vitamin A levels in patients with CF are influenced by the inflammatory response

scientific article published in August 2004

Whole genome sequencing reveals the emergence of a Pseudomonas aeruginosa shared strain sub-lineage among patients treated within a single cystic fibrosis centre

scientific article published on 30 August 2018

Whole-Genome Sequences of Five Burkholderia pseudomallei Isolates from Australian Cystic Fibrosis Patients

scientific article

Within-Host Evolution of Burkholderia pseudomallei during Chronic Infection of Seven Australasian Cystic Fibrosis Patients

scientific article

Within-host evolution of Burkholderia pseudomallei over a twelve-year chronic carriage infection

scientific article published on 16 July 2013

Within-host whole genome analysis of an antibiotic resistant Pseudomonas aeruginosa strain sub-type in cystic fibrosis

scientific article

Work environment risks for health care workers with cystic fibrosis

article