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List of works by Francis Mccormack

A 25-year-old man with fatigue, dyspnea, and pulmonary cysts

scientific article published in January 2015

A Novel Quantitative Computed Tomographic Analysis Suggests How Sirolimus Stabilizes Progressive Air Trapping in Lymphangioleiomyomatosis

scientific article published on 22 January 2016

A Phase II Clinical Trial of an Aromatase Inhibitor for Postmenopausal Women with Lymphangioleiomyomatosis.

scientific article published on June 2017

Accuracy of chest high-resolution computed tomography in diagnosing diffuse cystic lung diseases.

scientific article published on 9 July 2015

Air travel in women with lymphangioleiomyomatosis.

scientific article

Alanine mutagenesis of surfactant protein A reveals that lipid binding and pH-dependent liposome aggregation are mediated by the carbohydrate recognition domain.

scientific article published in November 1997

An atoll variant that mocks

scientific article published in July 2013

Automated algorithm for quantifying the extent of cystic change on volumetric chest CT: initial results in Lymphangioleiomyomatosis.

scientific article published in April 2009

Birt-Hogg-Dubé syndrome.

scientific article published in September 2013

Chest Computed Tomographic Image Screening for Cystic Lung Diseases in Patients with Spontaneous Pneumothorax Is Cost Effective

scientific article published on 13 October 2016

Clinical predictors of mortality and cause of death in lymphangioleiomyomatosis: a population-based registry.

scientific article published on 25 September 2012

Clinical trials for rare lung diseases: lessons from lymphangioleiomyomatosis.

scientific article

Correction of pulmonary abnormalities in Sftpd-/- mice requires the collagenous domain of surfactant protein D.

scientific article

Crystallographic Complexes of Surfactant Protein A and Carbohydrates Reveal Ligand-induced Conformational Change

scientific article

Deletion mapping of N-terminal domains of surfactant protein A. The N-terminal segment is required for phospholipid aggregation and specific inhibition of surfactant secretion.

scientific article published in January 1999

Diagnosis and Treatment of Lymphatic Plastic Bronchitis in Adults Using Advanced Lymphatic Imaging and Percutaneous Embolization

scientific article

Diagnostic potential of serum VEGF-D for lymphangioleiomyomatosis.

scientific article published on January 2008

Differential Ligand Binding Specificities of the Pulmonary Collectins Are Determined by the Conformational Freedom of a Surface Loop.

scientific article published on 18 July 2017

Diffuse Cystic Lung Disease as the Presenting Manifestation of Sjögren Syndrome

scientific article

Diffuse Cystic Lung Disease. Part I.

scientific article

Diffuse Cystic Lung Disease. Part II.

scientific article

Domains of surfactant protein A that affect protein oligomerization, lipid structure and surface tension.

scientific article

Efficacy and Safety of Long-Term Sirolimus Therapy for Asian Patients with Lymphangioleiomyomatosis

scientific article

Eight novel variants in the SLC34A2 gene in pulmonary alveolar microlithiasis

scientific article published on 27 February 2020

Elucidation of Lipid Binding Sites on Lung Surfactant Protein A Using X-ray Crystallography, Mutagenesis, and Molecular Dynamics Simulations

scientific article

Endobronchial Carcinoid Tumor in an HIV-infected Patient

scientific article published in April 2010

Everolimus for the treatment of lymphangioleiomyomatosis: a phase II study

scientific article published on 25 June 2015

Expression and characterization of rat surfactant protein A synthesized in Chinese hamster ovary cells.

scientific article published on October 1990

Immunosuppressed surfactant protein A-deficient mice have increased susceptibility to Pneumocystis carinii infection

scientific article published on 15 February 2001

Interactions of pulmonary collectins with Bordetella bronchiseptica and Bordetella pertussis lipopolysaccharide elucidate the structural basis of their antimicrobial activities

scientific article published on December 2004

Kaposiform lymphangiomatosis, a newly characterized vascular anomaly presenting with hemoptysis in an adult woman

scientific article published in January 2014

Keratinocyte growth factor administration attenuates murine pulmonary mycobacterium tuberculosis infection through granulocyte-macrophage colony-stimulating factor (GM-CSF)-dependent macrophage activation and phagolysosome fusion

scientific article

Keratinocyte growth factor augments pulmonary innate immunity through epithelium-driven, GM-CSF-dependent paracrine activation of alveolar macrophages

scientific article

Keratinocyte growth factor supports pulmonary innate immune defense through maintenance of alveolar antimicrobial protein levels and macrophage function

scientific article published on 26 February 2016

Lymphangioleiomyomatosis - a wolf in sheep's clothing.

scientific article

Lymphangioleiomyomatosis screening in women with tuberous sclerosis.

scientific article published on August 2013

Lymphangioleiomyomatosis: A Monogenic Model of Malignancy

scientific article published on January 2017

Lymphangioleiomyomatosis: a clinical update.

scientific article

Lymphangioleiomyomatosis: calling it what it is: a low-grade, destructive, metastasizing neoplasm

scientific article published on December 2012

Lymphangioleiomyomatosis: insights about, and from, a rare disease

scientific article published on 01 December 2003

Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment.

scientific article published on 21 September 2012

Machine learning can predict disease manifestations and outcomes in lymphangioleiomyomatosis

scientific article published on 10 December 2020

Macrophage-independent fungicidal action of the pulmonary collectins

scientific article

Management of pneumothorax in lymphangioleiomyomatosis: effects on recurrence and lung transplantation complications.

scientific article

Microfibril-associated protein 4 binds to surfactant protein A (SP-A) and colocalizes with SP-A in the extracellular matrix of the lung.

scientific article published in August 2006

Modeling pulmonary alveolar microlithiasis by epithelial deletion of the Npt2b sodium phosphate cotransporter reveals putative biomarkers and strategies for treatment

scientific article

Molecular pathogenesis of lymphangioleiomyomatosis: lessons learned from orphans

scientific article

Mutagenesis of surfactant protein D informed by evolution and x-ray crystallography enhances defenses against influenza A virus in vivo

scientific article

Mutational analysis of Arg197 of rat surfactant protein A. His197 creates specific lipid uptake defects

scientific article published on 01 March 1998

Neither SP-A nor NH2-terminal domains of SP-A can substitute for SP-D in regulation of alveolar homeostasis.

scientific article

New concepts in collectin-mediated host defense at the air-liquid interface of the lung

scientific article

Nitric oxide production by rat alveolar macrophages can be modulated in vitro by surfactant protein A ⬇️

scientific article published on 01 June 1997

Nonmalignant Adult Thoracic Lymphatic Disorders.

scientific article

Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guidelines: Lymphangioleiomyomatosis Diagnosis and Management

scientific article published in September 2016

Oral administration of surfactant protein-a reduces pathology in an experimental model of necrotizing enterocolitis.

scientific article published on May 2015

Patient perspectives on management of pneumothorax in lymphangioleiomyomatosis.

scientific article published on May 2006

Pleural disease in lymphangioleiomyomatosis

scientific article published in June 2006

Prostaglandin-E2 Mediated Increase in Calcium and Phosphate Excretion in a Mouse Model of Distal Nephron Salt Wasting

scientific article published on 21 July 2016

Pulmonary Alveolar Microlithiasis

scientific article published on 24 June 2016

Pulmonary Vascular Shunts in Exercise-Intolerant Patients with Lymphangioleiomyomatosis

scientific article published on 01 November 2013

Pulmonary alveolar microlithiasis

scientific article published on 01 October 2013

Pulmonary alveolar microlithiasis

scientific article published on 27 November 2020

Pulmonary collectins selectively permeabilize model bacterial membranes containing rough lipopolysaccharide.

scientific article published on February 2006

Pulmonary manifestations of Birt-Hogg-Dubé syndrome.

scientific article published on September 2013

Pulmonary surfactant protein-A (SP-A) restores the surface properties of surfactant after oxidation by a mechanism that requires the Cys6 interchain disulfide bond and the phospholipid binding domain.

scientific article published on 24 February 2003

Rare Lung Diseases: Occasionally the "Horse" Has Stripes

scientific article published on 01 September 2016

Recurrent lymphangiomyomatosis after transplantation: genetic analyses reveal a metastatic mechanism.

scientific article

Regional Sparing in an Oligemic Lung Segment Supports Hematogenous Spread as a Pathogenic Mechanism in Lymphangioleiomyomatosis.

scientific article published on August 2015

Reply to: Treatment of Pulmonary Lymphangioleiomyomatosis During Pregnancy.

scientific article published on 22 January 2018

Reply: The ATS/JRS Guidelines on Lymphangioleiomyomatosis: Filling in the Gaps.

scientific article published on 13 March 2017

Review: Structural determinants of pattern recognition by lung collectins.

scientific article published on 27 April 2010

S-LAM in a man?

scientific article published on 01 July 2007

SP-R210 (Myo18A) Isoforms as Intrinsic Modulators of Macrophage Priming and Activation

scientific journal article

Screening for lymphangioleiomyomatosis by high-resolution computed tomography in young, nonsmoking women presenting with spontaneous pneumothorax is cost-effective

scientific article published on 18 February 2010

Serum VEGF-D a concentration as a biomarker of lymphangioleiomyomatosis severity and treatment response: a prospective analysis of the Multicenter International Lymphangioleiomyomatosis Efficacy of Sirolimus (MILES) trial

scientific article

Serum surfactant protein-A is a strong predictor of early mortality in idiopathic pulmonary fibrosis.

scientific article published on 02 March 2009

Site-directed mutagenesis of surfactant protein A reveals dissociation of lipid aggregation and lipid uptake by alveolar type II cells

scientific article published on 01 September 1998

Spontaneous Pneumothoraces in Patients with Birt-Hogg-Dubé Syndrome.

scientific article

Structure, processing and properties of surfactant protein A

scientific article published on 01 November 1998

Successful management of a chronic, refractory bronchopleural fistula with endobronchial valves followed by talc pleurodesis

scientific article published on 01 February 2014

Surfactant lipid peroxidation damages surfactant protein A and inhibits interactions with phospholipid vesicles

scientific article published on 16 March 2004

Surfactant protein A inhibits lipopolysaccharide-induced in vivo production of interleukin-10 by mononuclear phagocytes during lung inflammation.

scientific article published in March 2003

Surfactant protein A is a principal and oxidation-sensitive microbial permeabilizing factor in the alveolar lining fluid

scientific article published on 12 May 2005

Susceptibility of Hermansky-Pudlak mice to bleomycin-induced type II cell apoptosis and fibrosis.

scientific article published on 15 March 2007

The 85-kDa, arachidonic acid-specific phospholipase A2 is expressed as an activated phosphoprotein in Sf9 cells.

scientific article published on November 1993

The Cys6 intermolecular disulfide bond and the collagen-like region of rat SP-A play critical roles in interactions with alveolar type II cells and surfactant lipids

scientific article published in October 1997

The NHLBI lymphangioleiomyomatosis registry: characteristics of 230 patients at enrollment.

scientific article published on 06 October 2005

The alveolar epithelium determines susceptibility to lung fibrosis in Hermansky-Pudlak syndrome

scientific article

The collagen-like region of surfactant protein A (SP-A) is required for correction of surfactant structural and functional defects in the SP-A null mouse

scientific article published on 14 August 2001

The emergence of targetable MEKanisms in sporadic lymphatic disorders

scientific article published on 18 September 2020

The flagellum of Pseudomonas aeruginosa is required for resistance to clearance by surfactant protein A.

scientific article

The longer isoform and Cys-1 disulfide bridge of rat surfactant protein A are not essential for phospholipid and type II cell interactions.

scientific article published in November 1998

The way forward in lymphangioleiomyomatosis: a trial for every patient, every patient in a trial

scientific article published on 01 July 2011

Three-dimensional structure of rat surfactant protein A trimers in association with phospholipid monolayers.

scientific article published on May 2000

Two rat surfactant protein A isoforms arise by a novel mechanism that includes alternative translation initiation.

scientific article published in August 2000

Utility of [18F]2-fluoro-2-deoxyglucose-PET in sporadic and tuberous sclerosis-associated lymphangioleiomyomatosis.

scientific article

Utility of transbronchial biopsy in the diagnosis of lymphangioleiomyomatosis

scientific article

Vitamin D Deficiency and Reduced Lung Function in Connective Tissue-Associated Interstitial Lung Diseases ⬇️

scientific article published on August 5, 2010

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