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List of works by Johanna A Kremer Hovinga

A common origin of the 4143insA ADAMTS13 mutation

scientific article

A first case of congenital TTP on the African continent due to a new homozygous mutation in the catalytic domain of ADAMTS13.

scientific article

A functional single nucleotide polymorphism in the thrombin-activatable fibrinolysis inhibitor (TAFI) gene associates with outcome of meningococcal disease

article

A new tool to further explore the role of ADAMTS-13 in health and disease.

scientific article

ADAMTS-13, von Willebrand factor and related parameters in severe sepsis and septic shock

scientific article published on 22 August 2007

ADAMTS13 activity in sickle cell disease

scientific article published in July 2006

ADAMTS13 autoantibodies in patients with thrombotic microangiopathies and other immunomediated diseases

scientific article

ADAMTS13 gene variants and function in women with preeclampsia: a population- based nested case- control study from the HUNT Study.

scientific article published on 18 June 2015

Acquired thrombotic thrombocytopenic purpura: ADAMTS13 activity, anti-ADAMTS13 autoantibodies and risk of recurrent disease

scientific article published on 01 February 2008

Acute pancreatitis and thrombotic thrombocytopenic purpura.

scientific article

Blood group O and black race are independent risk factors for thrombotic thrombocytopenic purpura associated with severe ADAMTS13 deficiency

scientific article

Caplacizumab Treatment for Acquired Thrombotic Thrombocytopenic Purpura

scientific article published on 24 January 2019

Caplacizumab for Acquired Thrombotic Thrombocytopenic Purpura

scientific article

Caplacizumab reduces the frequency of major thromboembolic events, exacerbations and death in patients with acquired thrombotic thrombocytopenic purpura

scientific article published on 26 April 2017

Case 13: Deep leg vein thrombosis due to acquired thrombophilia – Hyperhomocysteinemia caused by hitherto undiagnosed celiac disease

scientific article published on 01 September 1999

Cellular Factor XIII, a Transglutaminase in Human Corneal Keratocytes

scientific article published on 27 November 2019

Children and adults with thrombotic thrombocytopenic purpura associated with severe, acquired Adamts13 deficiency: comparison of incidence, demographic and clinical features

scientific article

Circulating DNA and myeloperoxidase indicate disease activity in patients with thrombotic microangiopathies

scientific article

Clinical importance of ADAMTS13 activity during remission in patients with acquired thrombotic thrombocytopenic purpura

scientific article published on 13 September 2016

Clinical outcomes after platelet transfusions in patients with thrombotic thrombocytopenic purpura

scientific article

Cognitive deficits after recovery from thrombotic thrombocytopenic purpura

scientific article

Congenital dyserythropoietic anaemia type II (HEMPAS) and haemochromatosis

Congenital dyserythropoietic anaemia type II (HEMPAS) and haemochromatosis: a report of two cases

scientific article published on 01 October 2003

Consensus on the standardization of terminology in thrombotic thrombocytopenic purpura and related thrombotic microangiopathies.

scientific article

Current insights into thrombotic microangiopathies: Thrombotic thrombocytopenic purpura and pregnancy

scientific article

Current management of thrombotic thrombocytopenic purpura

scientific article

Decreasing frequency of plasma exchange complications in patients treated for thrombotic thrombocytopenic purpura-hemolytic uremic syndrome, 1996 to 2011.

scientific article

Designed ankyrin repeat proteins: a new approach to mimic complex antigens for diagnostic purposes?

scientific article

Development of a clinically significant ADAMTS13 inhibitor in a patient with hereditary thrombotic thrombocytopenic purpura

article

Diagnosis of thrombotic thrombocytopenic purpura among patients with ADAMTS13 Activity 10%-20.

scientific article published on 17 August 2017

Different disparities of gender and race among the thrombotic thrombocytopenic purpura and hemolytic-uremic syndromes

scientific article

Discrepant activity levels of von Willebrand factor-cleaving protease (ADAMTS-13) in congenital thrombotic thrombocytopenic purpura

scientific article published on 01 August 2003

Efficacy and safety of open-label caplacizumab in patients with exacerbations of acquired thrombotic thrombocytopenic purpura in the HERCULES study

scientific article published on 09 December 2019

Elevated levels of plasma prekallikrein, high molecular weight kininogen and factor XI in coronary heart disease

scientific article published in April 2002

Estimation of Nuwiq® (simoctocog alfa) activity using one-stage and chromogenic assays-Results from an international comparative field study

scientific article published on 20 May 2019

Evidence for a role of anti-ADAMTS13 autoantibodies despite normal ADAMTS13 activity in recurrent thrombotic thrombocytopenic purpura

scientific article

Familial acquired thrombotic thrombocytopenic purpura: ADAMTS13 inhibitory autoantibodies in identical twins

scientific article

Fatal congenital thrombotic thrombocytopenic purpura with apparent ADAMTS13 inhibitor: in vitro inhibition of ADAMTS13 activity by hemoglobin

scientific article

Frequency and significance of HIV infection among patients diagnosed with thrombotic thrombocytopenic purpura

scientific article

Genetic variations in complement factors in patients with congenital thrombotic thrombocytopenic purpura with renal insufficiency

scientific article

Hereditary Thrombotic Thrombocytopenic Purpura

scientific article published on 01 October 2019

Hereditary thrombotic thrombocytopenic purpura and the hereditary TTP registry.

scientific article

High prevalence of hereditary thrombotic thrombocytopenic purpura in central Norway: from clinical observation to evidence.

scientific article

Hyperbilirubinemia interferes with ADAMTS-13 activity measurement by FRETS-VWF73 assay: diagnostic relevance in patients suffering from acute thrombotic microangiopathies

scientific article published on 01 April 2007

Immunoadsorption and autologous transplantation for life-threatening primary antiphospholipid syndrome

scientific article published on 01 September 2019

Impaired DNase1-mediated degradation of neutrophil extracellular traps is associated with acute thrombotic microangiopathies.

scientific article

Improving on nature: redesigning ADAMTS13.

scientific article

Indications for a protective function of beta2-glycoprotein I in thrombotic thrombocytopenic purpura

scientific article

Initial experience from a double-blind, placebo-controlled, clinical outcome study of ARC1779 in patients with thrombotic thrombocytopenic purpura

scientific article published on 24 February 2012

Is factor V Leiden a risk factor for thrombotic microangiopathies without severe ADAMTS13 deficiency?

scholarly article by Soraya Krieg et al published 2005 in Thrombosis and Haemostasis

Late onset and pregnancy-induced congenital thrombotic thrombocytopenic purpura

scientific article

Long-term Kidney Outcomes in Patients With Acquired Thrombotic Thrombocytopenic Purpura

scientific article published on 21 June 2017

Massive muscle haematoma three months after starting vitamin K antagonist therapy for deep-vein thrombosis in an antithrombin deficient patient: Another case of factor IX propeptide mutation

scholarly article by Maximilian Jahns et al published 2011 in Thrombosis and Haemostasis

Measurement of ADAMTS-13 activity in plasma by the FRETS-VWF73 assay: comparison with other assay methods

scientific article published on 01 May 2006

Microangiopathic haemolytic anaemia in metastasizing malignant tumours is not associated with a severe deficiency of the von Willebrand factor-cleaving protease.

scientific article

Multiple B-cell clones producing antibodies directed to the spacer and disintegrin/thrombospondin type-1 repeat 1 (TSP1) of ADAMTS13 in a patient with acquired thrombotic thrombocytopenic purpura.

scientific article

Multiple major morbidities and increased mortality during long-term follow-up after recovery from thrombotic thrombocytopenic purpura

scientific article

Novel ADAMTS13 mutations in an obstetric patient with Upshaw-Schulman syndrome

scientific article

Obinutuzumab in two patients suffering from immune-mediated thrombotic thrombocytopenic purpura intolerant to rituximab

scientific article published on 09 August 2019

Pancreatitis preceding acute episodes of thrombotic thrombocytopenic purpura-hemolytic uremic syndrome: report of five patients with a systematic review of published reports

scientific article

Pathophysiology of thrombotic thrombocytopenic purpura and hemolytic uremic syndrome.

scientific article

Persistence of circulating ADAMTS13-specific immune complexes in patients with acquired thrombotic thrombocytopenic purpura

scientific article

Plasma DNA is Elevated in Patients with Deep Vein Thrombosis

scientific article published on October 2013

Plasma therapy in thrombotic thrombocytopenic purpura: review of the literature and the Bern experience in a subgroup of patients with severe acquired ADAMTS-13 deficiency

scientific article

Pregnancy outcomes following recovery from acquired thrombotic thrombocytopenic purpura

scientific article

Prevalence of Neuropsychiatric Symptoms and Stroke in Patients with Hereditary Thrombotic Thrombocytopenic Purpura

scientific article published on 18 May 2022

Progress in Haemostasis. From individual patients to pathophysiological insights.

scientific article

Recombinant ADAMTS-13: first-in-human pharmacokinetics and safety in congenital thrombotic thrombocytopenic purpura

scientific article published on 14 September 2017

Recombinant ADAMTS13 normalizes von Willebrand factor-cleaving activity in plasma of acquired TTP patients by overriding inhibitory antibodies.

scientific article

Relation between ADAMTS13 activity and ADAMTS13 antigen levels in healthy donors and patients with thrombotic microangiopathies (TMA).

scientific article

Relationship between in vitro lipopolysaccharide-induced cytokine response in whole blood, angiographic in-stent restenosis, and toll-like receptor 4 gene polymorphisms

scientific article published on 13 January 2005

Ribosomal and immune transcripts associate with relapse in acquired ADAMTS13-deficient thrombotic thrombocytopenic purpura

scientific article

Rituximab reduces risk for relapse in patients with thrombotic thrombocytopenic purpura

scientific article

Role of ADAMTS13 in the pathogenesis, diagnosis, and treatment of thrombotic thrombocytopenic purpura

scientific article

Schistocytic anaemia, severe thrombocytopenia, and renal dysfunction: thrombotic microangiopathy due to severe acquired ADAMTS-13 deficiency. Case 2.

scientific article

Second international collaborative study evaluating performance characteristics of methods measuring the von Willebrand factor cleaving protease (ADAMTS-13).

scientific article published on 26 July 2008

Soluble thrombomodulin in patients with established atherosclerosis

scientific article published on 01 January 2004

Splenectomy in relapsing and plasma-refractory acquired thrombotic thrombocytopenic purpura.

scientific article

Sporadic bloody diarrhoea-associated thrombotic thrombocytopenic purpura-haemolytic uraemic syndrome: an adult and paediatric comparison

scientific article

Successful liver transplantation in a child with acute-on-chronic liver failure and acquired thrombotic thrombocytopenic purpura.

scientific article

Survival and relapse in patients with thrombotic thrombocytopenic purpura

scientific article

Targeting anticoagulant protein S to improve hemostasis in hemophilia.

scientific article published on 9 January 2018

The International Hereditary Thrombotic Thrombocytopenic Purpura Registry: Key findings at enrolment until 2017

scientific article published on 21 February 2019

The Oklahoma Thrombotic Thrombocytopenic Purpura-Hemolytic Uremic Syndrome Registry: the Swiss connection

scientific article

The impact of congenital thrombotic thrombocytopenic purpura on pregnancy complications

scientific article published on 06 February 2014

The splenic autoimmune response to ADAMTS13 in thrombotic thrombocytopenic purpura contains recurrent antigen-binding CDR3 motifs.

scientific article

The von Willebrand factor-cleaving protease (ADAMTS-13) and the diagnosis of thrombotic thrombocytopenic purpura (TTP)

scientific article

Thromboembolism in patients with congenital afibrinogenaemia. Long-term observational data and systematic review

scientific article

Thrombophilia Impact on Treatment Decisions, Subsequent Venous or Arterial Thrombosis and Pregnancy-Related Morbidity: A Retrospective Single-Center Cohort Study

scientific article published in 2022

Thrombotic Thrombocytopenic Purpura and Hemolytic Uremic Syndrome

article published in 2017

Thrombotic microangiopathic syndromes associated with drugs, HIV infection, hematopoietic stem cell transplantation and cancer

scientific article

Thrombotic microangiopathies

scientific article published on 01 May 2013

Thrombotic thrombocytopenic pupura (TTP) dinner symposium proceedings

scientific article published on 22 June 2016

Thrombotic thrombocytopenic purpura

article

Thrombotic thrombocytopenic purpura

scientific article published on 01 August 2005

Thrombotic thrombocytopenic purpura

scientific article published on 01 January 2004

Thrombotic thrombocytopenic purpura--an often missed diagnosis

scientific article

Thrombotic thrombocytopenic purpura: diagnostic criteria, clinical features, and long-term outcomes from 1995 through 2015

scholarly article published 11 April 2017

Treatment of thrombotic thrombocytopenic purpura.

scientific article

Von Willebrand Factor Interacts with Surface-Bound C1q and Induces Platelet Rolling.

scientific article published on 3 October 2016

Von Willebrand factor-cleaving protease (ADAMTS-13) activity in thrombotic microangiopathies: diagnostic experience 2001/2002 of a single research laboratory.

scientific article

[Recurrent hepatitis in oral anticoagulation: coumarin-induced hepatitis]

scientific article published on 01 September 1999

von Willebrand factor-cleaving protease (ADAMTS-13) activity determination in the diagnosis of thrombotic microangiopathies: the Swiss experience

scientific article

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