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Authors whose works are in public domain in at least one jurisdiction

List of works by Elliott Vichinsky

A Phase 3 Randomized Trial of Voxelotor in Sickle Cell Disease

scientific article published on 14 June 2019

A Short-Term Trial of Butyrate to Stimulate Fetal-Globin-Gene Expression in the β-Globin Disorders ⬇️

scientific article published on January 14, 1993

A cautionary note regarding hydroxyurea in sickle cell disease

scientific article published on 01 February 1994

A comparison of conservative and aggressive transfusion regimens in the perioperative management of sickle cell disease. The Preoperative Transfusion in Sickle Cell Disease Study Group

scientific article published on 01 July 1995

A complication risk score to evaluate clinical severity of thalassaemia syndromes

scientific article published on 20 November 2020

A phase 1/2 trial of HQK-1001, an oral fetal globin inducer, in sickle cell disease

scientific article published on 07 August 2012

A pilot study of subcutaneous decitabine in β-thalassemia intermedia ⬇️

scientific article published on June 23, 2011

A pilot study of the short-term use of simvastatin in sickle cell disease: effects on markers of vascular dysfunction

scientific article published on 8 April 2011

A potent oral P‐selectin blocking agent improves microcirculatory blood flow and a marker of endothelial cell injury in patients with sickle cell disease ⬇️

scientific article published on April 10, 2012

A randomized, placebo-controlled trial of arginine therapy for the treatment of children with sickle cell disease hospitalized with vaso-occlusive pain episodes ⬇️

scientific article published on 03 May 2013

A simple model to assess and improve adherence to iron chelation therapy with deferoxamine in patients with thalassemia

scientific article

Advances in clinical research in sickle cell disease

scientific article published on 12 March 2008

Advances in the treatment of alpha-thalassemia ⬇️

scientific article published on April 1, 2012

Alloimmunization in sickle cell anemia and transfusion of racially unmatched blood

scientific article published in June 1990

Alpha thalassemia major--new mutations, intrauterine management, and outcomes

scientific article

American Society of Hematology 2020 guidelines for sickle cell disease: prevention, diagnosis, and treatment of cerebrovascular disease in children and adults

scientific article published on 01 April 2020

Anemia associated with rheumatoid arthritis ⬇️

scientific article published on 01 April 1979

Anemia in the newborn period

scientific article published on July 1, 1979

Application of Multiplex Ligation-Dependent Probe Amplification to Screen for β-Globin Cluster Deletions: Detection of Two Novel Deletions in a Multi Ethnic Population ⬇️

scientific article published on April 11, 2013

Approaches to transfusion therapy and iron overload in patients with sickle cell disease: results of an international survey

scientific article published on 30 July 2010

Arginine therapy: a new treatment for pulmonary hypertension in sickle cell disease?

scientific article published on 5 March 2003

Availability of related donors for bone marrow transplantation in sickle cell anemia

scientific article published in February 1994

Barriers to adherence of deferoxamine usage in sickle cell disease

scientific article published on May 2005

Barriers to bone marrow transplantation for sickle cell anemia.

scientific article published on May 1996

Bone and joint disease in sickle cell disease

scientific article

Bone mineral density in children with sickle cell anemia

scientific article published in December 2006

Butyrate analogues modulate globin gene expression in human and ovine erythroid cells

scientific article published on 01 January 1989

Can peak systolic velocities be used for prediction of stroke in sickle cell anemia?

scientific article published on 23 October 2004

Caregiving time in sickle cell disease: psychological effects in maternal caregivers

scientific article published in January 2007

Central venous catheter complications in sickle cell disease

scientific article

Changes in the epidemiology of thalassemia in North America: a new minority disease

scientific article

Changing patterns of thalassemia worldwide

scientific article

Characterization of low bone mass in young patients with thalassemia by DXA, pQCT and markers of bone turnover ⬇️

scientific article published on April 5, 2011

Chart Card: Feasibility of a Tool for Improving Emergency Department Care in Sickle Cell Disease ⬇️

scientific article published on November 1, 2010

Chelation use and iron burden in North American and British thalassemia patients: a report from the Thalassemia Longitudinal Cohort ⬇️

scientific article published on January 25, 2012

Chlamydia pneumoniae and acute chest syndrome in patients with sickle cell disease

scientific article published on January 2003

Chronic organ failure in adult sickle cell disease.

scientific article published in December 2017

Chronic pulmonary disorders in sickle cell disease: findings at thin-section CT.

scientific article published in December 1994

Clinical Manifestations of -Thalassemia ⬇️

scientific article published on May 1, 2013

Clinical application of deferasirox: practical patient management

scientific article published on May 2008

Clinical evaluation of avascular necrosis in patients with sickle cell disease: Children's Hospital Oakland Hip Evaluation Scale--a modification of the Harris Hip Score

scientific article

Clinical events in the first decade in a cohort of infants with sickle cell disease. Cooperative Study of Sickle Cell Disease ⬇️

scientific article published on July 15, 1995

Combined chelation therapy with deferasirox and deferoxamine in thalassemia ⬇️

scientific article published on November 11, 2012

Comprehensive care in sickle cell disease: its impact on morbidity and mortality

scientific article published on July 1991

Concurrent sickle-cell anemia and alpha-thalassemia: effect on severity of anemia

scientific article published on 01 February 1982

Contraceptive use in the chronically ill adolescent female

scientific article published on 01 January 1988

Core decompression in avascular necrosis of the hip in sickle-cell disease

scientific article published in June 1996

Current treatment of sickle cell disease

scientific article published on 01 October 1980

Darbepoetin alfa for the treatment of anaemia in alpha- or beta- thalassaemia intermedia syndromes

scientific article published on 18 April 2011

Deferiprone and hepatic fibrosis

scientific article (publication date: 15 June 2003)

Detection and assessment of stroke in patients with sickle cell disease: neuropsychological functioning and magnetic resonance imaging

scientific article

Detection of Hb E/β-Thalassemia Versus Homozygous EE Using High-Performance Liquid Chromatography Results from Newborns ⬇️

scientific article published on February 1, 1993

Dietary nonheme iron is equally bioavailable from ferritin or ferrous sulfate in thalassemia intermedia

scientific article published on 12 December 2017

Differences in the prevalence of growth, endocrine and vitamin D abnormalities among the various thalassaemia syndromes in North America

scientific article

Differentiation of homozygous hemoglobin E from compound heterozygous hemoglobin E-beta O-thalassemia by hemoglobin E mutation analysis

scientific article published on May 1, 1992

Discontinuing penicillin prophylaxis in children with sickle cell anemia. Prophylactic Penicillin Study II.

scientific article

Diseases of iron metabolism

scientific article

Disparity in the management of iron overload between patients with sickle cell disease and thalassemia who received transfusions

scientific article

Distinct HLA associations by stroke subtype in children with sickle cell anemia

scientific article (publication date: April 2003)

Dose-escalation study of ICA-17043 in patients with sickle cell disease

scientific article published in November 2006

Dysregulated arginine metabolism and cardiopulmonary dysfunction in patients with thalassaemia

scientific article

Dysregulated arginine metabolism, hemolysis-associated pulmonary hypertension, and mortality in sickle cell disease

scientific article

Education and employment status of children and adults with thalassemia in North America

scientific article

Effect of Inhaled Cannabis for Pain in Adults With Sickle Cell Disease: A Randomized Clinical Trial

scientific article published on 01 July 2020

Effect of hydroxyurea on growth in children with sickle cell anemia: results of the HUG-KIDS Study

scientific article published in February 2002

Effect of hydroxyurea on mortality and morbidity in adult sickle cell anemia: risks and benefits up to 9 years of treatment

scientific article

Effects of a long-term transfusion regimen on sickle cell-related illnesses

scientific article published in December 1994

Efficacy and safety of deferasirox compared with deferoxamine in sickle cell disease: two-year results including pharmacokinetics and concomitant hydroxyurea

scientific article published on 19 September 2013

Efficacy and safety of deferasirox doses of >30 mg/kg per d in patients with transfusion-dependent anaemia and iron overload

scientific article published on 18 September 2009

Elevated exhaled carbon monoxide concentration in hemoglobinopathies and its relation to red blood cell transfusion therapy

scientific article

Elevated fasting breath hydrogen and abnormal hydrogen breath tests in children with sickle cell disease: a preliminary report

scientific article published in April 1989

Elevated tricuspid regurgitant jet velocity in subgroups of thalassemia patients: insight into pathophysiology and the effect of splenectomy

scientific article published on 28 February 2014

Emergency department utilization by Californians with sickle cell disease, 2005-2014.

scientific article published on 21 December 2016

Emerging 'A' therapies in hemoglobinopathies: agonists, antagonists, antioxidants, and arginine

scientific article published on January 1, 2012

Emerging therapy in hemoglobinopathies: lessons from the past and optimism for the future

scientific article

Encephaloduroarteriosynangiosis (EDAS) in young patients with cerebrovascular complications of sickle cell disease: Single-institution experience

scientific article published on 22 May 2017

Epidemiologic and clinical characteristics of nontransfusion-dependent thalassemia in the United States.

scientific article published on 10 April 2018

Erythrocyte glutamine depletion, altered redox environment, and pulmonary hypertension in sickle cell disease

scientific article

Ethical issues and risk/benefit assessment of iron chelation therapy: advances with deferiprone/deferoxamine combinations and concerns about the safety, efficacy and costs of deferasirox [Kontoghiorghes GJ, Hemoglobin 2008; 32(1-2):1-15.].

scientific article

Evaluation of Mandible Fractures in Patients With Sickle Cell Anemia-A Nationwide Study

scientific article published on 03 January 2019

Evidence for the presence of CFU-E with increased in vitro sensitivity to erythropoietin in sickle cell anemia

scientific article published on 01 May 1984

Experience with newborn screening using isoelectric focusing.

scientific article published in May 1989

F reticulocyte response in sickle cell anemia treated with recombinant human erythropoietin: a double-blind study

scientific article

Favorable outcomes after in utero transfusion in fetuses with alpha thalassemia major: a case series and review of the literature

scientific article published on 9 November 2016

Fertility and Pregnancy in Women with Transfusion-Dependent Thalassemia

scientific article published in April 2018

Fertility in transfusion-dependent thalassemia men: effects of iron burden on the reproductive axis

scientific article

Fertility potential in thalassemia major women: current findings and future diagnostic tools

scientific article published on August 2010

Fetal Hb production during acute erythroid expansion. I. Observations in patients with transient erythroblastopenia and post-phlebotomy

scientific article published on 01 April 1980

Fetal haemoglobin augmentation in E/beta(0) thalassaemia: clinical and haematological outcome

scientific article

First report of reversal of organ dysfunction in sickle cell anemia by the use of hydroxyurea: splenic regeneration.

scientific article published on September 1996

Fracture prevalence and relationship to endocrinopathy in iron overloaded patients with sickle cell disease and thalassemia

scientific article published on 15 March 2008

Gene Therapy in Patients with Transfusion-Dependent β-Thalassemia

article

Growth retardation in sickle-cell disease treated by nutritional support

scientific article published on 01 April 1985

HLA type and risk of alloimmunization in sickle cell disease

scientific article

Hb E/beta-thalassaemia: a common & clinically diverse disorder ⬇️

scientific article published on October 1, 2011

HbE/β-Thalassemia: Basis of Marked Clinical Diversity ⬇️

scientific article published on December 1, 2010

Hematologic problems in immigrants from Southeast Asia

scientific article

Hematopoietic hormones: from cloning to clinic

scientific article

Hemoglobin E-beta-thalassemia: Progress report from the International Study Group

scientific article

Hemoglobin H-constant spring in North America: an alpha thalassemia with frequent complications

scientific article

Hemoglobin Hakkari: an autosomal dominant form of beta thalassemia with inclusion bodies arising from de novo mutation in exon 2 of beta globin gene

scientific article published in February 2010

Hemoglobin e syndromes

scientific article

Hemoglobinopathies

scientific article published in November 2008

Hemolysis-associated pulmonary hypertension in thalassemia

scientific article

Heterogeneity of hemoglobin H disease in childhood

scientific article published in February 2011

Highlight article: Vincristine-induced anemia in hereditary spherocytosis

scientific article published on 04 June 2019

Human T cell lymphotropic virus type 1 infection among U.S. thalassemia patients

scientific article published on 12 March 2013

Human T-cell lymphotropic virus type 1 infection among U.S. Thalassemia patients.

scientific article published on 7 January 2014

Hydroxycarbamide-induced changes in E/beta thalassemia red blood cells

scientific article

Hydroxyurea and arginine therapy: impact on nitric oxide production in sickle cell disease

scientific article published in August 2003

Identifying Clinical and Research Priorities in Sickle Cell Lung Disease. An Official American Thoracic Society Workshop Report

scientific article published on 01 September 2019

Immune response after splenectomy

scientific article published on January 1978

In utero hematopoietic cell transplantation for hemoglobinopathies

scientific article

Inadequate dietary intake in patients with thalassemia

scientific article

Inadequate erythroid response to hypoxia in cystic fibrosis

scientific article published on 01 July 1984

Increased leucocyte apoptosis in transfused β‐thalassaemia patients ⬇️

scientific article published on December 6, 2012

Inflammation and oxidant-stress in beta-thalassemia patients treated with iron chelators deferasirox (ICL670) or deferoxamine: an ancillary study of the Novartis CICL670A0107 trial

scientific article published on 10 May 2008

Influence of sickle cell disease on susceptibility to HIV infection

scientific article published on 08 April 2020

Invasive pneumococcal infections in children with sickle cell disease in the era of penicillin prophylaxis, antibiotic resistance, and 23-valent pneumococcal polysaccharide vaccination

scientific article

Iron Deficiency: Implications Before Anemia

scientific article published on 01 January 2021

Iron chelation adherence to deferoxamine and deferasirox in thalassemia

scientific article

Iron deficiency in health and disease

scientific article published on January 1, 1983

Iron homeostasis during transfusional iron overload in beta-thalassemia and sickle cell disease: changes in iron regulatory protein, hepcidin, and ferritin expression.

scientific article published in June 2007

Iron metabolism and iron chelation in sickle cell disease

scientific article

Is the medical home for adult patients with sickle cell disease a reality or an illusion?

scientific article published on 25 March 2015

Lifespan care in SCD: Whom to transition, the patients or the health care system?

scientific article published on 17 February 2017

Liver ferritin subunit ratios in neonatal hemochromatosis

scientific article published in April 2003

Liver transplantation in a child with sickle cell anemia

scientific article published on 01 May 1995

Long-term follow-up and booster immunization with polyvalent pneumococcal polysaccharide in patients with sickle cell anemia

scientific article published on 01 August 1984

Long-term safety and efficacy of deferasirox (Exjade) for up to 5 years in transfusional iron-overloaded patients with sickle cell disease

scientific article

Long-term safety and efficacy of deferasirox in young pediatric patients with transfusional hemosiderosis: Results from a 5-year observational study (ENTRUST).

scientific article published on 10 March 2017

Longitudinal changes in brain magnetic resonance imaging findings in children with sickle cell disease

scientific article published in April 2002

Low dose, oral epsilon aminocaproic acid for renal papillary necrosis and massive hemorrhage in hemoglobin SC disease.

scientific article published in January 2010

Lower alloimmunization rates in pediatric sickle cell patients on chronic erythrocytapheresis compared to chronic simple transfusions ⬇️

scientific article published on April 23, 2012

Managing sickle cell disease ⬇️

scientific article published on November 15, 2003

Measuring chromosome breaks in patients with thalassemia

scientific article published in January 2005

Morbidity and mortality in chronically transfused subjects with thalassemia and sickle cell disease: A report from the multi-center study of iron overload

scientific article published in April 2007

Multidisciplinary approach to pain management in sickle cell disease

scientific article published on 01 January 1982

Mycoplasma disease and acute chest syndrome in sickle cell disease

scientific article published on July 2003

Natural history of blood pressure in sickle cell disease: risks for stroke and death associated with relative hypertension in sickle cell anemia

scientific article published in February 1997

Neuropsychological dysfunction and neuroimaging abnormalities in neurologically intact adults with sickle cell anemia

scientific article

New advances in the pathophysiology and management of sickle cell disease

scientific article published on March 1, 1994

New therapies and approaches to transfusion in sickle cell disease in children.

scientific article

New therapies in sickle cell disease

scientific article

Newborn screening for hemoglobinopathies in California

scientific article published on April 2009

Newborn screening for sickle cell disease: 4 years of experience from California's newborn screening program

scientific article

Newborn screening for sickle cell disease: effect on mortality

scientific article

Non-transfusion-dependent thalassemia and thalassemia intermedia: epidemiology, complications, and management

scientific article

Non-transfusion-dependent thalassemias ⬇️

scientific article published on June 1, 2013

Novel influenza A (H1N1) viral infection in pediatric patients with sickle-cell disease

scientific article

Novel therapeutic approaches in sickle cell disease

scientific article

Oral iron chelators and the treatment of iron overload in pediatric patients with chronic anemia

scientific article

Ototoxicity in hemoglobinopathy patients chelated with desferrioxamine

scientific article published in February 1996

Outcomes of preimplantation genetic diagnosis therapy in treatment of beta-thalassemia: A retrospective analysis

scientific article

Pain in sickle cell disease. Rates and risk factors

scientific article published on 01 July 1991

Pain in thalassaemia: the effects of age on pain frequency and severity ⬇️

scientific article published on December 30, 2012

Pain over time and its effects on life in thalassemia ⬇️

scientific article published on November 1, 2013

Pancytopenia induced by hypothermia

scientific article

Patient-reported outcomes of deferasirox (Exjade, ICL670) versus deferoxamine in sickle cell disease patients with transfusional hemosiderosis. Substudy of a randomized open-label phase II trial

scientific article

Peroxidation, vitamin E, and sickle-cell anemia

scientific article published on 01 January 1982

Phospholipase A2 levels in acute chest syndrome of sickle cell disease

scientific article

Physical therapy alone compared with core decompression and physical therapy for femoral head osteonecrosis in sickle cell disease. Results of a multicenter study at a mean of three years after treatment

scientific article

Pituitary iron and factors predictive of fertility status in transfusion dependent thalassemia

scientific article published on 29 October 2020

Population based surveillance in sickle cell disease: methods, findings and implications from the California registry and surveillance system in hemoglobinopathies project (RuSH).

scientific article published on 30 August 2014

Preface to Cooley's Anemia: Ninth Symposium

scientific article

Pregnancy outcomes in women with thalassemia in North America and the United Kingdom

scientific article

Prevalence of HFE mutations in California newborns

scientific article published in September 2006

Prophylaxis with oral penicillin in children with sickle cell anemia. A randomized trial

scientific article published on 01 June 1986

Pulmonary complications

scientific article

Pulmonary complications of sickle cell disease

scientific article published on 01 November 2008

Pulmonary fat embolism: a distinct cause of severe acute chest syndrome in sickle cell anemia

scientific article published on 01 June 1994

Pulmonary hypertension and NO in sickle cell

scientific article published on August 2010

Pulmonary hypertension in hemolytic anemias

scientific article published on 11 February 2010

Pulmonary hypertension in sickle cell disease.

scientific article published in February 2004

Pulmonary hypertension in thalassemia

scientific article

Quality of life in patients with thalassemia intermedia compared to thalassemia major

scientific article

Red cell alloimmunization in a diverse population of transfused patients with thalassaemia ⬇️

scientific article published on February 17, 2011

Relationship between chronic transfusion therapy and body composition in subjects with thalassemia

scientific article

Relative response of patients with myelodysplastic syndromes and other transfusion-dependent anaemias to deferasirox (ICL670): a 1-yr prospective study

scientific article

Renal medullary carcinoma in an adolescent with sickle cell anemia ⬇️

scientific article published on September 24, 2013

Reproductive capacity in iron overloaded women with thalassemia major

scientific article

Response to "efficacy and safety of sildenafil for the treatment of severe pulmonary hypertension in patients with hemoglobinopathies: results from a long-term follow up " Haematologica 2014;99(2):e17-18.

scientific article published on February 2014

Risk factors and mortality associated with an elevated tricuspid regurgitant jet velocity measured by Doppler-echocardiography in thalassemia: a Thalassemia Clinical Research Network report ⬇️

scientific article published on July 19, 2011

Risk of recurrent stroke in patients with sickle cell disease treated with erythrocyte transfusions

scientific article published on 01 June 1995

Safety and efficacy of deferiprone for pantothenate kinase-associated neurodegeneration: a randomised, double-blind, controlled trial and an open-label extension study

scientific article published on 01 July 2019

Safety and efficacy of pegylated interferon alpha-2a and ribavirin for the treatment of hepatitis C in patients with thalassemia

scientific article published on 12 June 2008

Serotype-specific immunoglobulin G antibody responses to pneumococcal polysaccharide vaccine in children with sickle cell anemia: effects of continued penicillin prophylaxis

scientific article published on 01 December 1996

Serum ferritin level changes in children with sickle cell disease on chronic blood transfusion are nonlinear and are associated with iron load and liver injury

scientific article published on 31 August 2009

Severe sickle cell disease--pathophysiology and therapy

scientific article published on 09 October 2009

Sickle Cell Anemia and Related Hemoglobinopathies ⬇️

scientific article published on May 1, 1980

Sickle cell disease in a patient with sickle cell trait and compound heterozygosity for hemoglobin S and hemoglobin Quebec-Chori

scientific article

Sickle cell disease.

scientific article published on 15 March 2018

Sickle-cell disease not identified by newborn screening because of prior transfusion

scientific article published on 01 February 2000

Sildenafil therapy in thalassemia patients with Doppler-defined risk of pulmonary hypertension ⬇️

scientific article published on April 12, 2013

Simvastatin reduces vaso-occlusive pain in sickle cell anaemia: a pilot efficacy trial

scientific article

Single and combination drug therapy for fetal hemoglobin augmentation in hemoglobin E-beta 0-thalassemia: Considerations for treatment

scientific article

Sodium butyrate enhances fetal globin gene expression in erythroid progenitors of patients with Hb SS and beta thalassemia

scientific article published on 01 July 1989

Stroke recurrence in adult sickle cell patients: it is time for action!

scientific article

Suggested guidelines for the treatment of children with sickle cell anemia.

scientific article

Surgery and anesthesia in sickle cell disease. Cooperative Study of Sickle Cell Diseases ⬇️

scientific article published on November 15, 1995

The diagnosis of iron deficiency anemia in sickle cell disease ⬇️

scientific article published on 01 November 1981

The effect of whole body vibration therapy on bone density in patients with thalassemia: A pilot study ⬇️

scientific article published on 07 August 2012

The mediating effects of family functioning on psychosocial outcomes in healthy siblings of children with sickle cell disease

scientific article published on 25 February 2011

The palatability and tolerability of deferasirox taken with different beverages or foods ⬇️

scientific article published on April 23, 2013

The role of fetal hemoglobin-enhancing agents in thalassemia

scientific article

The spectrum of brain MR abnormalities in sickle-cell disease: a report from the Cooperative Study of Sickle Cell Disease

scientific article published on 01 May 1996

Transfusion and chelation practices in sickle cell disease: a regional perspective

scientific article published on 30 July 2010

Transfusion complications in thalassemia patients: a report from the Centers for Disease Control and Prevention (CME).

scientific article published on 25 July 2013

Transfusional iron burden and liver toxicity after bone marrow transplantation for acute myelogenous leukemia and hemoglobinopathies

scientific article published in February 2008

Treatment of Classic Pantothenate Kinase–Associated Neurodegeneration with Deferiprone and Intrathecal Baclofen ⬇️

scientific article published on August 1, 2013

Treatment of heart failure in adults with thalassemia major: response in patients randomised to deferoxamine with or without deferiprone

scientific article published on 20 May 2013

Treatment of hepatitis C virus infection in thalassemia

scientific article

Universal screening for hemoglobinopathies using high-performance liquid chromatography: clinical results of 2.2 million screens.

scientific article published in January 1994

Unstable hemoglobins, hemoglobins with altered oxygen affinity, and m-hemoglobins.

scientific article

Using qualitative and quantitative strategies to evaluate knowledge and perceptions about sickle cell disease and sickle cell trait

scientific article published on May 2006

Using quality improvement strategies to enhance pediatric pain assessment

scientific article published in February 2002

Validation and reliability of a disease-specific quality of life measure (the TranQol) in adults and children with thalassaemia major

scientific article

Variability of homozygous sickle cell disease: The role of alpha and beta globin chain variation and other factors

scientific article

Vitamin C deficiency in patients with sickle cell anemia.

scientific article

Zinc supplementation improves bone density in patients with thalassemia: a double-blind, randomized, placebo-controlled trial ⬇️

scientific article published on August 14, 2013

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