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Calpastatin-mediated inhibition of calpains in the mouse brain prevents mutant ataxin 3 proteolysis, nuclear localization and aggregation, relieving Machado-Joseph disease

scientific article published in August 2012

Author/s

author: Nicole Déglon, Carlos B. Duarte, Luis Pereira De Almeida, Nélio Gonçalves, Sebastian Kügler

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Work details

Publication date
August 1, 2012
- -
Language
English

Copyright status